13 results
Kawasaki Disease (Mucocutaneous Lymph Node Syndrome) 
An rare systemic acute febrile vasculitic syndrome. Aetiology unknown. 
Affects
acute febrile vasculitic ... Affects children ... #Features #Signs ... #Symptoms #Diagnosis ... #Peds #Pediatrics
Neuromyelitis Optica (NMO) - Clinical Manifestations
 • Optic neuritis: Reduced visual acuity, ranging from mild to
NMO) - Clinical Manifestations ... Motor and sensory deficits ... #Optica #NMO #Manifestations ... diagnosis #neurology #symptoms ... #signs
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
) - Affects the ... : • Behçet Syndrome ... • Cogan Syndrome ... Presentation - Systemic Symptoms ... purpura: strong sign
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... M > F Clinical Manifestations ... meningitis), MCC CNS symptoms ... diagnosis #management #signs ... #symptoms #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Presentation: Systemic Symptoms ... purpura: Strong sign ... • Progressive symptoms ... • Behcet syndrome ... • Cogan syndrome
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Butterfly rash, Vasculitis ... Restrictive lung defect ... Demyelinating syndromes ... erythematosus #signs ... #symptoms #diagnosis
Neurological Manifestations of Tuberculosis
Spinal Arachnoiditis & Polyradiculopathy:
 • Subacute onset of limb weakness, bladder/bowel dysfunction, muscle
Neurological Manifestations ... lesion Pott's Disease ... Reconstitution Inflammatory Syndrome ... Meningitis • Include: vasculitis ... focal neurological deficits
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Cryofibrinogenemia Symptoms ... malignancies, vasculitis ... Cryofibrinogenemia Clinical Manifestations ... Antiphospholipid syndrome ... #rheumatology #hematology
Chagas Disease - American Trypanosomiasis - Diagnosis and Management Summary
Chagas disease (American trypanosomiasis) is an infectious
Cutaneous manifestations ... Romana's sign ... Indeterminate form (No signs ... /symptoms, positive ... IFA) assays to detect
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
Overwhelming clinical syndrome ... most frequently affects ... age, however the disease ... Diagnosis: HLH signs ... and symptoms can