25 results
Clinical Disease Characteristics and Suggested Algorithm for Diagnostic Evaluation of Patients With Symptoms of Polymyalgia Rheumatica

#Diagnosis
Clinical Disease ... and Suggested Algorithm ... #Diagnosis #Rheumatology ... #Algorithm #GCA ... GiantCell #Temporal #Arteritis
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... Behcet syndrome (Clinical ... SLE, Reactive arthritis ... Syndrome #diagnosis #management ... signs #symptoms #rheumatology
Behcet's Syndrome - Treatment
Ulcers:
 • Treatment: Topical steroids
 • Prevention: Colchicine
 • Azathioprine for refractory disease
Arthritis:
Arthritis: • Colchicine ... for refractory lesions ... or refractory lesions ... Syndrome #Treatment #management ... #pharmacology #rheumatology
Giant Cell Arteritis (GCA) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Visual Symptoms/Loss or
Giant Cell Arteritis ... ) - Vasculitis Management ... Algorithm - ACR ... GCA #Vasculitis #Management ... #rheumatology
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Clinical triad ... Fever, Arthralgia/arthritis ... #diagnosis #management ... #treatment #rheumatology
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Somatic) Syndrome Clinical ... chondritis, skin lesions ... thromboembolic disease ... • giant cell arteritis ... Autoinflammatory #Somatic #rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
GPA causes disease ... Rarely dominate the clinical ... • Giant cell arteritis ... Polyangiitis #GPA #dermatology ... rash #diagnosis #rheumatology
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Clinical Features ... of hip (rare), Arthritis ... Cranial nerve lesions ... pain (20%) Renal disease ... symptoms #diagnosis #rheumatology
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Group for Behget's Disease ... ulcers - Ocular disease ... test Most Common Clinical ... vasculitis) • Arthritis ... Diagnosis #criteria #rheumatology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
juvenile idiopathic arthritis ... fever syndromes Clinical ... Fever is the main clinical ... Syndrome #Diagnosis #Management ... #Hematology #Rheumatology