40 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
• Urogenital Lesions ... ) • Cutaneous Lesions ... 75%): acneiform lesions ... #diagnosis #management ... signs #symptoms #rheumatology
Behcet's Syndrome - Treatment
Ulcers:
 • Treatment: Topical steroids
 • Prevention: Colchicine
 • Azathioprine for refractory disease
Arthritis:
Behcet's Syndrome ... for refractory lesions ... or refractory lesions ... #Treatment #management ... #pharmacology #rheumatology
Management of Lupus Nephritis
Lupus nephritis (LN) in 10 to 40% of SLE
Hallmark = proteinuria 20.5 g/g
active and chronic lesions ... (C) : chronic lesions ... IV (A) : active lesions ... (C) : chronic lesions ... #rheumatology #
Idiopathic Inflammatory Myopathies - 
Dermatomyositis (DM), Immune-Mediated Necrotizing Myopathy (IMNM), Antisynthetase Syndrome (ASS), Inclusion Body Myositis
Antisynthetase Syndrome ... Idiopathic #Myopathy #Comparison ... #Managment #algorithm ... #Rheumatology #
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... vasculitis - Skin lesions ... variety of skin lesions ... joints) • Vascular lesions ... Diagnosis #criteria #rheumatology
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Cranial nerve lesions ... Demyelinating syndromes ... , Aortic valve lesions ... symptoms #diagnosis #rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
vasculitis Skin lesions ... • Painful skin lesions ... Papulo-necrotic lesions ... reticularis • Necrotic lesions ... gangrene Skin lesions
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Clinical Syndrome ... chondritis, skin lesions ... myelodysplastic syndrome ... myelodysplastic syndrome ... Autoinflammatory #Somatic #rheumatology
Multiple Myeloma and Monoclonal Gammopathies
C - HyperCalcemia- calcium > 11 mg/dL / >1 mg/dL the ULN
R
LLN B - Bony lesions ... 100 • >1 focal lesions ... plasmacytoma, POEMs syndrome ... MGUS #diagnosis #hematology
Optic Neuritis - Diagnosis and Management
 • Epidemiology: Female (75%), 18-50 years,
caucasian
 • Symptoms: Moderate visual
Diagnosis and Management ... focal, anterior lesions ... Brain: normal / WM lesions ... Neuritis #Diagnosis #Management ... #treatment #rheumatology