9 results
CNS Manifestations of Systemic Lupus Erythematosus (SLE)

Clinical Manifestations: Demyelinating Syndrome, Headache, Movement disorders, Seizure disorders, Aseptic
Headache, Movement disorders ... , Seizure disorders ... Encephalopathy, Cognitive Dysfunction ... inflammation, leading ... cerebritis #diagnosis #management
Lymphomas and Lymphoproliferative Disorders - Differential Diagnosis Algorithm
Hodgkin Lymphoma ~40% - Characteristic For Reed-Sternberg (RS) Cells
Lymphoproliferative Disorders ... Differential Diagnosis Algorithm ... #Classification ... pathophysiology #Hematology ... #differential #algorithm
Hypoxemia / Hypoxia - Rapid Response Management Algorithm

Stridor - Upper airway pathology:
 • Anaphylaxis
 • Foreign
Rapid Response Management ... Algorithm Stridor ... • Vocal cord dysfunction ... Hypoventilation: • CNS ... Neuromuscular disorders
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
IL-1 and IL-6, leading ... nervous system (CNS ... ) dysfunction • ... Syndrome #Diagnosis #Management ... #Hematology #Rheumatology
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
Skin Disease Classification ... ) • Endocrine disorders ... involve PNS and CNS ... mild cognitive dysfunction ... , and mood disorder
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
- Organ dysfunction ... progressive organ dysfunction ... Thyroid (Riedel's), CNS ... complement • Classification ... #Rheumatology
Cyclic Vomiting Syndrome (CVS) - Management Algorithm
General Approach:
 - Identify and avoid triggers
 - Good sleep
Vomiting Syndrome (CVS ... ) - Management Algorithm ... Comorbidities (psychiatric disorders ... use, autonomic dysfunction ... #Algorithm #Treatment
Langerhans Cell Histiocytosis (LCH)

Granulomatous Lesions comprising langerin-positive histiocytes and an inflammatory infiltrate can arise in virtually
LCH is a rare disorder ... various tissues, leading ... • Endocrine Dysfunction ... CNS involvement: ... Histiocytosis #Diagnosis #Management
Essential Thrombocythemia (ET)
ET is a chronic myeloproliferative neoplasm. Most cases are related to mutations that affect
hemoproliferative disorder ... • Treatment algorithms ... patients with no CV ... #diagnosis #management ... #hematology