20 results
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
disease: Uveitis ... or retinal vasculitis ... test Most Common Clinical ... , retinal vasculitis ... Diagnosis #criteria #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... vasculitis) • ... (SVC/IVC occlusion ... Behcet syndrome (Clinical ... signs #symptoms #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
, and ocular inflammation ... ulcers, cutaneous, ocular ... Syndrome: - Ocular ... reactions, and vaso-occlusive ... differential #diagnosis #rheumatology
Transient Monocular Vision loss - Differential Diagnosis
Ischemia	
 - Large artery disease (atherothrombosis, embolus, dissection).
  -
- Large artery disease ... - Small artery occlusive ... disease (anterior ... optic neuropathy, vasculitis ... Ocular causes -
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Cryoglobulinemia Vasculitis ... not related to clinical ... l) : Vascular occlusion ... arthritis • Renal ... #Diagnosis #Rheumatology
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... pulmonary emboli, and ocular ... thrombi including retinal ... and/or venous occlusions ... Diagnosis: • + Clinical
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis ... Clinical manifestations ... with purpura - Renal ... with refractory disease ... #Rheumatology #
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
pulmonary and renal ... reactions, and vaso-occlusive ... , and ocular inflammation ... Cogan syndrome: Ocular ... Differential #Diagnosis #Rheumatology
Susac Syndrome - Clinical Triad
 - Central nervous system dysfunction
 - Branch retinal artery occlusion
 -
Susac Syndrome - Clinical ... dysfunction - Branch retinal ... artery occlusion ... - Recurrent disease ... Diagnosis #Management #Rheumatology
Diagnosis of IgA Vasculitis (Henoch-Schönlein Purpura) - French Vasculitis Study Group 

1) Suggestive clinical manifestations
1) Suggestive clinical ... individuals - Clinical ... complications - Renal ... - Systemic disease ... HSP #Diagnosis #Rheumatology