1782 results
Hemophilia - Diagnosis and Management
Diagnosis:
 • Consistent bleeding history (unless screening for disease in family members
Hemophilia - Diagnosis ... screening for disease ... with established disease ... • Establish hemophilia ... those with severe disease
Summary of Coagulation Deficiencies
Inherited:
 • Hemophilia A - Deficiency of Factor VIII
 • Hemophilia B -
Inherited: • Hemophilia ... Factor VIII • Hemophilia ... Malabsorption (e.g. celiac disease ... Advanced Liver Disease
Hemophilia
#Management #Peds #HemophiliaA #HemophiliaB #PEMSource
Hemophilia #Management ... #Peds #HemophiliaA ... #HemophiliaB #PEMSource
Vascular Joint Pain - Differential Diagnosis Algorithm 
 - Constant Pain (Ischemia)
 - Acute Onset
 -
Peripheral Vascular Disease ... Hemarthrosis (Hemophilia
Causes of Knee Effusions - Differential Diagnosis Framework

Knee Effusion Red Flags:
1. Fever/Chills/Joint pain/Night sweats/Weight loss
	- DDX:
		-
- Systemic disease ... Gonorrhea - Lyme’s disease ... SLE - Behcet Disease ... Hemarthrosis - Hemophilia ... - Sickle cell disease
Treatment of Bleeding in Selected Inherited Disorders of Hemostasis

#Bleeding #Disorders #HemophiliaA #HemophiliaB #Management #Table #Treatment
Bleeding #Disorders #HemophiliaA ... #HemophiliaB #Management
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
- Bone marrow disease ... deficiency • Liver disease ... • Hemophilia ... Von Willebrand disease ... Dermatosis: Schamberg Disease
Causes of Post-Partum Hemorrhage - Differential Diagnosis Algorithm
Blood Loss: >500mL post vaginal delivery OR >1000 mL
von Willebrand's disease ... , Hemophilia A)
Von Willebrand Disease Classification
Type 1 (Accounts for ~3/4 of cases):
 • Defect: Quantitative defect (i.e. not
Von Willebrand Disease ... Clinically similar to hemophilia ... VonWillebrand #Disease
Factor VIII synthesis - Normal, Haemophilia A and Von Willebrand Disease

Normal - vWF carrier protein protects
synthesis - Normal, Haemophilia ... Von Willebrand Disease ... Haemophilia A - ... Von Willebrand Disease ... VonWillebrand #Disease