16 results
Hyperviscosity Syndrome - Causes and Treatment

 - Waldenstrom macroglobulinemia (most common) / Plasmapheresis 
 - Multiple
Hyperviscosity Syndrome ... MetroHealth_EM #Hyperviscosity
Hyperviscosity-Related Retinopathy in Waldenström’s Macroglobulinemia Funduscopic examination revealed bilateral retinal-vein dilatation and tortuosity with retinal hemorrhages
Hyperviscosity-Related ... #Hemorrhages #Hyperviscosity
Priapism 

Secondary Causes:
Medications- intracavernosal injections, anticoagulants, PDE5 inhibitors, alpha blockers, methylphenidate, cocaine
Any hyperviscosity syndrome (SCD, leukemia,
, cocaine Any hyperviscosity
Mesenteric Ischemia - Differential Diagnostic Schema
Chronic: ASCVD, Venous, Vasculitides 5% (PAN, [E]GPA, IgA, MPA)
Acute
 - Venous
disorder, Malignancy, Hyperviscosity
Cryoglobulinemia Classification Types

Type 1: Monoclonal IgM (rarely IgG/lgA)
 • Raynaud phenomenon, Digital ulcers/gangrene, Livedo reticularis, Hyperviscosity
Livedo reticularis, Hyperviscosity
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
extremities • Hyperviscosity
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
Manifestations: • Hyperviscosity ... gap • CRAB • Hyperviscosity
Transient Monocular Vision loss - Differential Diagnosis
Ischemia	
 - Large artery disease (atherothrombosis, embolus, dissection).
  -
age, DM, HTN), hyperviscosity
Oncologic Emergencies - Differential Diagnosis Framework

HEMATOLOGIC ONCOLOGIC EMERGENCIES:
Hyperviscosity Syndrome:
 • Spontaneous bleeding
 • Shortness of breath
EMERGENCIES: Hyperviscosity
Leukostasis vs Tumor Lysis Syndrome
Leukostasis:
 • Pathophysiology: Large, immature blasts and high WBC count cause hyperviscosity
WBC count cause hyperviscosity