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Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Management of Hypocomplementemic ... Urticarial Vasculitis ... HUV 1) Chronic urticaria ... vasculitis 3) Hypocomplementemia ... #Urticarial #Vasculitis
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Pathophysiology of Hypocomplementemic ... Urticarial Vasculitis ... TerrierBen #Hypocomplementemic ... #Urticarial #Vasculitis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
often involved • Hypocomplementemic ... Urticarial Vasculitis ... Vasculitis): - Urticaria ... and hypocomplementemia ... cryoglobulinemia, urticarial
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Elevated AST ALT • Hypocomplementemia ... : Urticarial Vasculitis ... Vasculitis) • Hypocomplementemic ... Urticarial Vasculitis ... maculopapular lesions, urticaria
Causes of Hypocomplementemia - CHAMPS Mnemonic
C - Cryoglobulinemia (85%), C3 glomerulopathy, cirrhosis
H - Heavy Chain deposition
Causes of Hypocomplementemia ... @AnnKumfer #Hypocomplementemia
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
Cold Urticaria Prevalence ... Chronic spontaneous urticaria ... Chronic inducible urticarias ... .14674 #Cold #Urticaria
Severe Urticarial Skin Rash on Physical Exam

#Urticarial #Skin #Rash #PhysicalExam #clinical #video #dermatology #urticaria
Severe Urticarial ... Physical Exam #Urticarial ... #dermatology #urticaria
Urticaria Mimics

Conditions That May Be Confused with Urticaria

Arthropod bites 
, Atopic dermatitis 
, Bullous pemphigoid 
,
Urticaria Mimics ... Confused with Urticaria ... Pityriasis rosea , Urticaria ... #Differential #Urticaria
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
bullae, Ulceration, Urticaria ... - Anti-C1q (Urticarial
Urticaria (hives): Skin reaction that occurs in response to cold, food allergies, meds, environmental exposures, stings,
infections
Urticaria (hives ... Dermatology #SkinRash #Urticaria