10 results
Hemophagocytic Lymphohistiocytosis (HLH)
Definition: Overwhelming clinical syndrome associated with excessive macrophage activation and cytokine storm due to
: Overwhelming clinical ... syndrome associated ... : HLH signs and ... • Infection should ... antibiotic therapy should
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
common in Asia • HLA-B51 ... association • M > F Clinical ... (Clinical Dx). ... retinal tears, Ischemia ... #signs #symptoms
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Diagnosis Framework ... : • Purpura, ischemic ... Differential Diagnosis ... purpura: Strong sign ... proximal muscles of shoulder
Venous Thrombosis vs Arterial Thrombosis - Differential Diagnosis Framework

VENOUS THROMBOSIS

 • Acquired Risk Factors:
	- >48 hours
- Differential Diagnosis ... • Nephrotic Syndrome ... , Ischemic Liver ... antibodies (APLS should ... 19 - PNH - Vasculitis
Causes of Secondary Hypertension - Workup and Differential Diagnosis
Approach (when evaluation should be done):
1. Severe or
and Differential Diagnosis ... when evaluation should ... 109 mm Hg) with clinical ... renal bruit or signs ... Coarctation of aorta, Vasculitis
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
HLH is a critical ... syndrome, a search ... Clinical Presentation ... • Common Signs ... #Management #Hematology
Vancomycin induced Leukocytoclastic Vasculitis (LCV) of the Hand
70 M vertebral osteomyelitis on vancomycin and cefepime for
Diagnosis? ... antiphospholipid syndrome ... Churg-Strauss syndrome ... Hand #skinrash #dermatology ... #clinical #photo
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
malignancies, vasculitis ... Cryofibrinogenemia Clinical ... limb and bowel ischemia ... : • + Clinical ... Antiphospholipid syndrome
Transverse Myelitis Overview

Focal inflammatory disorder of the spinal cord resulting in rapid onset of weakness, sensory
Transverse Myelitis - Clinical ... • Bilateral signs ... NMO-IgG (anti-AQP4) should ... , MOG-IgG test should ... - Sjogren - Vasculitis
Takayasu’s Arteritis: Pathogenesis and clinical findings

 - Fatigue, weight loss, low grade fever, arthralgias
 - Incr
Pathogenesis and clinical ... Acute Coronary Syndrome ... asymmetrical (common) - Ischemic ... Takayasus #Arteritis #Vasculitis ... #Diagnosis #Signs