19 results
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
• Pauci-immune vasculitis ... • Goodpasture syndrome ... vasculitis (inflamed ... Polyangiitis #GPA #dermatology ... rash #diagnosis #rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Granulomatosis with ... Polyangiitis (MPA) - ANCA Vasculitis ... @MithuRheum #Granulomatosis ... Polyangiitis #MPA #ANCA #Vasculitis ... Guidelines #algorithm #rheumatology
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
ANCA-positive vasculitis ... (Eosinophilic granulomatosis ... polyangiitis, Granulomatosis ... ANCA-negative vasculitis ... Investigations • Labs: CBC
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
- Wegener granulomatosis ... Churg-Strauss syndrome ... - Schnitzler syndrome ... - Sjögren syndrome ... Vessels #Diagnosis #Rheumatology
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Eosinophilic Granulomatosis ... (EGPA) - ANCA Vasculitis ... Daily Oral GC CYC ... #Eosinophilic #Granulomatosis ... Guidelines #algorithm #rheumatology
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
cases • Sjögren syndrome ... ANCA-Associated Vasculitis ... ANCA+ 90% • Granulomatosis ... Renal-limited vasculitis ... antibodies #diagnosis #rheumatology
Autoantibodies and their Disease Associations
ANA - Non-specific; common in SLE, autoimmune hepatitis
Anti-CCP, Rheumatoid factor - RA
Anti-dsDNA
La) - Sjogren's syndrome ... disease c-ANCA - Vasculitis ... Wegener's granulomatosis ... p-ANCA - Vasculitis ... diagnosis #table #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
glomerulonephritis - Granulomatous ... (Granulomatous ... : • Behçet Syndrome ... • Cogan Syndrome ... Lab Tests: • CBC
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
(GRANULOMATOUS ... Mucocutaneous lymph node syndrome ... • Behcet syndrome ... • Cogan syndrome ... Differential #Diagnosis #Rheumatology
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... (AAV): GPA (granulomatous ... (eosinophilic granulomatosis ... palpable purpura 2/2 vasculitis ... coagulopathy) • CBC