12 results
Jaundice and Kayser-Fleischer Rings in Wilson's Disease

#Jaundice #Kayser #Fleischer #Rings #Wilsons #Disease #clinical #video #ocular #physicalexam
Jaundice and Kayser-Fleischer ... Rings in Wilson's ... Disease #Jaundice ... #Disease #clinical ... video #ocular #physicalexam
Clinical Examination for Liver and Biliary Diseases
1) Hands: Clubbing, Dupuytren's contracture, Leuconychia, Bruising, Flapping tremor (hepatic
erythema 2) Face: Jaundice ... Xanthelasma and jaundiced ... Kayser-Fleischer rings in Wilson's ... Edema #biliary #physicalexam ... #cirrhosis #liver
Common Etiologies of Cirrhosis

Inflammation

 - Hepatitis B (15 percent)

 - Hepatitis C (47 percent)

 - Schistosomiasis
Etiologies of Cirrhosis ... Schistosomiasis - Autoimmune ... Primary biliary cirrhosis ... - Wilson disease ... Venoocclusive disease
Elevated Liver Enzymes - Differential Diagnosis Algorithm
Severe ALT > 15x ULN
 • Viral
 • Drugs/Toxins
 •
• Ischemia • Autoimmune ... • Wilson's ... • Drugs • Wilson's ... • Cholestatic disease ... Infiltrative • Cirrhosis
Primary Biliary Cirrhosis - Diagnosis Algorithm
Symptoms: Fatigue, Pruritus, Right upper quadrant discomfort
Signs: Jaundice, Xanthelasmata, Hepatomegaly
Associated history:
Primary Biliary Cirrhosis ... discomfort Signs: Jaundice ... of associated autoimmune ... disease (e.g. dryness ... disease, Persistent
Clinical Diagnosis of Autoimmune Hepatitis
 - Onset of jaundice within prior 8 weeks
 - Ongoing consumption
Clinical Diagnosis of Autoimmune ... Hepatitis - Onset of jaundice ... metabolic liver disease ... (Wilson disease ... SMA >1:80 #Autoimmune
Hepatomegaly - Differential Diagnosis Algorithm
Malignant
 • Primary Carcinoma
 • Metastases
 • Lymphoma
 • Leukemia
 • Polycythemia
Hemochromatosis • Wilson's ... Disease • Amyloidosis ... Hepatitis • Autoimmune ... Primary Biliary Cirrhosis
Primary Biliary Cirrhosis (PBC) - Summary

PBC Epidemiology:
 • Female:Male 9:1
 • Common European descent
 • Age:
Primary Biliary Cirrhosis ... Pathophysiology: • T lymphocyte ... cholestasis → Cirrhosis ... hyperpigmentation • Jaundice ... but elevated as disease
Primary Sjogren’s Syndrome: Pathogenesis and Clinical Findings
• Primary Sjögren's is a solitary process whereas secondary Sjögren's
accompanies other autoimmune ... diseases • In ... primary biliary cirrhosis ... with systemic diseases ... Symptoms: - Lymphocyte
Acute Liver Injury - Differential Diagnosis Algorithm

Vascular Causes of Acute Liver Injury: 
 • Hepatic vein:
Metabolic/Hereditary: Wilson ... , Celiac disease ... • Autoimmune: ... Autoimmune hepatitis ... hepatitis: < 1 • Cirrhosis