27 results
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Dermatologic Manifestations ... Rarely dominate the clinical ... • Fungal infections ... vasculitis #Dermatologic ... Polyangiitis #GPA #dermatology
Cutaneous manifestations associated with myelodysplastic syndrome
 • Myeloid hemopathy with the most frequent skin lesions (20%)
most frequent skin ... appearing during the disease ... differential #diagnosis #dermatology ... #oncology #clinical ... #skin
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Systemic amyloidosis, Nodular ... Cold agglutinin disease ... manifestations #dermatology ... #skin #clinical
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Clinical triad ... Arthralgia/arthritis, Skin ... • Ocular: uveitis ... #diagnosis #management
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... ulceration • Ocular ... response to local skin ... Behcet syndrome (Clinical ... Syndrome #diagnosis #management
Blastomycosis (Blastomyces): Gilchrist’s disease, Chicago disease - Summary Sheet
 • Morphology
 • Geography, Reservoir and Mode
transmission: aerogenic, skin ... inoculation • Clinical ... Diagnosis • Management ... Blastomyces #diagnosis #management ... #summary #fungal
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Cryofibrinogenemia Clinical ... pulmonary emboli, and ocular ... Diagnosis: • + Clinical ... Warfarin-induced skin ... #rheumatology #hematology
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• Heavy Chain disease ... Alpha & Mu) Skin ... thrombosis+Pulm HTN+skin ... Sneddon-Wilkinson disease ... Differential #Diagnosis #Oncology
Mycoses

HISTOPLASMOSIS
• Inhalation of conidia → Yeast → travel to lymph nodes → spread in body
• Bird
has five major clinical ... osteomyelitis or skin ... stain of clinical ... osteoarticular, pulmonary, ocular ... #Diagnosis #Management
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
Rheumatic pain Clinical ... Diagnosis: • A clinical ... disease. ... Rheumatology #diagnosis #management ... #Dermatology