18 results
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Clinical triad ... TMA • Cardiac: pericarditis ... Pulmonary: pleural effusion ... diagnosis #management #treatment ... #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... : Pericarditis, ... Behcet syndrome (Clinical ... Arthritis, AS Treatment ... signs #symptoms #rheumatology
Leptospirosis
Pathogen: Leptospira (interrogans, kirschneri, noguchii)
Risk Factors:
 • Occupational exposure - Farmers, ranchers, trappers, veterinarians
 • Recreational
: conjunctival suffusion ... Severe pulmonary disease ... Epidemiologic exposure + clinical ... agglutination - test ... microbiology #diagnosis #treatment
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Clinical Features ... 50%): Pleurisy / effusion ... syndromes Heart (25%): Pericarditis ... pain (20%) Renal disease ... symptoms #diagnosis #rheumatology
Hepatopulmonary Syndrome - Diagnosis and Management Summary
A defect in arterial oxygenation due to a gas exchange
intrinsic lung disease ... shunt (Type 2) Clinical ... 10 minutes of rest ... ) on room air Treatment ... diagnosis #management #treatment
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... Clinical history ... specific laboratory tests ... IgG4 #Related #Disease ... #rheumatology
Evaluation of suspected incomplete Kawasaki Disease

1. AHA consensus recommendations
2. Infants ≤6 months old on day ≥7
incomplete Kawasaki Disease ... if they have no clinical ... regurgitation, pericardial effusion ... echo is positive, treatment ... those >day 10 with clinical
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
) Suspect: Clinical ... Non-autoimmune rheumatologic ... lymphoproliferative syndrome Clinical ... Lungs: • Pleural effusions ... • Asymptomatic pericarditis
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
life-threatening diseases ... anti-GBM) Other tests ... o infection • Echocardiogram ... LVEF, pericardial effusion ... diagnosis #management #treatment
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Clinical suspicion ... the extent of disease ... Amyloidosis Clinical ... Persistent pleural effusions ... Testing: • EKG • Echocardiogram