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Diagnosis and management of Polyarteritis Nodosa (PAN)

Chapel Hill 2012 definition: 
Necrotizing vasculitis ofmedium or small arteries
definition: Necrotizing ... vasculitis ofmedium ... glomerulonephritis or vasculitis ... involvement French Vasculitis ... Diagnosis #Management #Vasculitis
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
semiology of Cutaneous Vasculitis ... • Drug-induced vasculitis ... SLE +++ • IgA vasculitis ... (10%) • Necrotizing ... vasculitis (5%)
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... When to Consider Vasculitis ... SMALL VESSEL VASCULITIS ... MPO > PR3 - Necrotizing ... PR3-ANCA) - Necrotizing
Red Leg - Cellulitis Mimickers
 - Unilateral
     • Contact Dermatitis
Nodosum • Vasculitis ... Infectious • Necrotizing
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
disease via: • Necrotizing ... • Pauci-immune vasculitis ... Granulomatous vasculitis ... inflammation) • Necrotising ... vasculitis, extravascular
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... A group of necrotizing ... , small-vessel vasculitis ... Levamisole-induced vasculitis ... ANCA #Associated #Vasculitis
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Vasculitis - Differential ... When to Consider Vasculitis ... abnormalities Vasculitis ... Symptoms (SX) in Vasculitis ... have PR3-ANCA) • Necrotizing
Weakness - Differential Diagnosis Framework

Approach To Weakness:
 • Non-neuromuscular disorder (Cardiac, pulmonary etc)
 • CNS ->
Inflammatory: Vasculitis ... multiplex (DM, Vasculitis-polyarteritis ... Immune mediated necrotizing ... anti-Jo-1] - (Vasculitis ... dystrophies, or vasculitis
Hemoptysis - Differential Diagnosis Framework
Massive Hemoptysis: >150-300 mL in 24h
Airway disease: 
 • Bronchitis, Bronchiectasis, Malignancy
Bacterial (TB, Necrotizing ... Autoimmune: ANCA-Assoc vasculitis
Rheumatoid arthritis (RA): Extra-articular manifestations
Skin: 
 • Inflammation of skin (esp. over areas of stress) forms
stress) forms large necrotizing ... blood vessels (vasculitis