10 results
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Polyangiitis (MPA) - ANCA ... Vasculitis Management ... RTX, GC+CYC, GC+AZA ... Polyangiitis #MPA #ANCA ... #Treatment #ACR2021
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Polyangiitis (EGPA) - ANCA ... Vasculitis Management ... GC + MTX, GC + AZA ... #Polyangiitis #ANCA ... #Treatment #ACR2021
Systemic Lupus Erythematosus (SLE) - Diagnosis and Management Summary
 • Epidemiology: 10-180/100,000, Typically Age 20-40, F:M
Diagnosis and Management ... Workup: - ANA ... 50-60% - pANCA ... life-threatening • Treatment ... Usual therapeutic management
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
Workup: - ANA ... constitutional symptoms • Treatment ... Workup: - ANA ... life-threatening • Treatment ... Usual therapeutic management
Systemic Lupus Erythematosus - Summary
Antinuclear (ANA) - 95% - Initial screening test
Anti-dsDNA - 50%
 • Associated
Antinuclear (ANA ... • Specific for SLE ... severe disease Treatment ... Erythematosus #SLE ... #rheumatology #management
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Summary Autoimmune ANCA ... Auto-antibodies: ANCA ... Renal #Syndromes #differential ... #diagnosis #management ... #treatment
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
Behcet disease) Differential ... Oral aphthae : SLE ... • Arthritis: SLE ... Arthritis, AS Treatment ... Syndrome #diagnosis #management
Posterior Reversible Encephalopathy Syndrome (PRES) Overview

Clinico-Radiological Syndrome, characterized by:
 • Headache
 • Seizures
 • Altered mental
circulation: MCA ACA ... Reversible course Differential ... epilepticus Treatment ... underlying cause • Treatment ... Syndrome #diagnosis #management
Drug Induced Lupus (DIL)
 • Epidemiology: -10% of all lupus cases, drug-dependent, 4:1 to 1:1 F:M
is rare in DIL, SCLE-DIL ... Workup: - ANA ... constitutional symptoms • Treatment ... rheumatology #diagnosis #treatment ... #management
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
cases such as: • SLE ... Nonspecific ↑ ESR, CRP, ANA ... affected tissue Treatment ... rheumatology #diagnosis #management