29 results
Castleman's Disease and Associated Syndromes
HYALINE VASCULAR VARIANT
 • unicentric, HHV8-ve, children and young.
 • Hyalinized vessels
Castleman's Disease ... associated with Castleman's ... disorders (myeloma, POEMS ... faheema_hasan #Castlemans
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
macroglobulinosis • POEMS ... syndrome • DADS-M • POEMS ... Involvement: • POEMS ... component+neuropathy+Castleman
Multiple Myeloma and Monoclonal Gammopathies
C - HyperCalcemia- calcium > 11 mg/dL / >1 mg/dL the ULN
R
plasmacytoma, POEMs ... syndrome, Castleman's
#POEMS syndrome
#POEMS syndrome
TAFRO

TAFRO syndrome was first described in 2010, standing for:
- Thrombocytopenia
- Anasarca
- Fever
- Reticulin fibrosis
- Organomegaly

TAFRO syndrome
of multicentric Castleman ... syndrome (SFTS) - POEMS
Elevated Globulin - Protein Gap (Total Protein - Albumin > 4)

Work-up of an Elevated Globulin Gap:
•
skin changes (POEMS ... plasmacytoma • Castleman
Pathology - Castleman disease. 

Mediastinal mass in a younger woman.

Histologic Features of Castleman disease, hyaline vascular
Pathology - Castleman ... Histologic Features of Castleman ... @mjcascio #Castleman
Having a Mental Block remembering HeartBlocks? Check out this fun poem/infographic from @nurseslabs!
#Diagnosis #Cardiology #EKG #ECG
Check out this fun poem
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Cytokine secretion: POEMS
Monoclonal Gammopathy of Clinical Significance (MGUS) - Differential Diagnosis

Neurologic-Centered:
 (+) Systemic Features: POEMS, AL amyloid, Cryoglobulinemia
Systemic Features: POEMS ... xanthogranuloma (NXG) • POEMS