70 results
Staphylococcal Scalded Skin Syndrome (SSSS) 
(aka Ritter disease)

#Staphylococcal #Scalded #Skin #Syndrome #SSSS #Diagnosis #Pediatrics #Dermatology #Ritter
Staphylococcal Scalded Skin ... (aka Ritter disease ... Syndrome #SSSS #Diagnosis ... #Pediatrics #Dermatology ... #Ritter #Disease
A schema of the pathophysiology of the inborn errors of metabolism, excluding complex storage diseases. Helps
complex storage diseases ... the lab values table ... , UpToDate #Pediatrics ... Pathophysiology #Diagnosis ... #Table #IEM #NICU
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
ulceration • Ocular ... response to local skin ... retinal damage) • Skin ... test (this is a skin ... inhibitors • Uveitis- Ophthalmology
Sickle Cell Disease and the Eye 

Ocular Manifestations of Sickle Cell Disease

 - Hyphema is Dangerous
Sickle Cell Disease ... and the Eye Ocular ... Manifestations #Ocular ... #Eye #Ophthalmology ... #Diagnosis
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome - Diagnosis ... Diagnostic Criteria ... vasculitis - Skin ... Wide variety of skin ... #Diagnosis #criteria
Extrapulmonary manifestations of sarcoidosis.
a. Endobronchial cobblestones (a nodular appearance of the tracheal wall mucosa). 
b. Diffuse
earlobe due to skin ... Perthes—Jüngling disease ... lesion of the skin ... manifestations #clinical #photo ... #diagnosis
Highlighted Conditions With Arteritis or Periarteritis of the Coronaries
Takayasu's arteritis:
 - Onset < 40 yrs
 -
Polyarteritis nodosa: - Skin ... Ulceration GI tract - Ocular ... IgG4-related disease ... #Differential #Diagnosis ... #Cardiology #Table
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Arthralgia/arthritis, Skin ... Differential Diaqnoses ... • Ocular: uveitis ... #diagnosis #management
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
trigger - Direct skin ... 50% of patients Skin ... Disorientation, vertigo Diagnostic ... Cold #Urticaria #diagnosis ... rheumatology #comparison #table
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
- Differential Diagnosis ... , and ocular inflammation ... ulcers, cutaneous, ocular ... Syndrome: - Ocular ... Differential Diagnosis