15 results
Cutaneous Manifestations of Monoclonal Gammopathy
 • Extravascular lg Deposits: Systemic amyloidosis, Nodular amyloidosis, Macroglobulinoderma, Follicular hyperkeratotic
Deposits: Systemic amyloidosis ... , Nodular amyloidosis ... Acquired cutis laxa ... , TEMPI syndrome ... dermatology #skin #clinical
Amyloidosis - Summary
Group of disorders associated with extracellular deposition of fibrils formed from low-molecular-weight proteins in
Clinical suspicion ... Clinical Manifestations ... : • Nephrotic syndrome ... Testing: • EKG • Echocardiogram ... disproportionate atrial
Antiphospholipid Syndrome (APS)
APS is a rare autoimmune disorder characterized by recurring blood clots resulting from antibodies
Antiphospholipid Syndrome ... anticoagulant (LA ... at least: • 1 clinical ... presence of 1 clinical ... present Treatment (EULAR
Amyloidosis on POCUS Echocardiogram - Apical 4 Chamber (A4C)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... Patient has water ... Cardiac #POCUS #clinical ... #Echocardiogram
Amyloidosis on POCUS Echocardiogram - Subcostal 4 Chamber (S4C)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... Patient has water ... Cardiac #POCUS #clinical ... #Echocardiogram
Amyloidosis on POCUS Echocardiogram - Parasternal long axis (PLAX)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... Patient has water ... Cardiac #POCUS #clinical ... #Echocardiogram
Amyloidosis on POCUS Echocardiogram - Parasternal short axis (PSAX)
Pt with systemic AL amyloidosis presents with 1
Echocardiogram ... thickening and biatrial ... Patient has water ... Cardiac #POCUS #clinical ... #Echocardiogram
Stiff Person Syndrome (SPS) - Diagnosis and Management Summary

Epidemiology:
 • Prevalence: 1-2 cases per million -
(SPS) - Diagnosis ... Clinical Manifestations ... EMG testing Lab ... - People with SPS ... #SPS #Diagnosis
Hepatopulmonary Syndrome (HPS) demonstrated on Echocardiogram Bubble Study

Intra-cardiac shunt: Bubbles appear in LA quickly (within 3
(HPS) demonstrated ... on Echocardiogram ... Bubbles appear in LA ... #Syndrome #Echocardiogram ... Bubble #Study #clinical
Cryofibrinogenemia Summary

Cryofibrinogenemia Epidemiology:
 • 40-70 years with a modest female predominance

Cryofibrinogenemia:
 • The precipitation of a
Cryofibrinogenemia Clinical ... pulmonary emboli, and ocular ... including retinal arterial ... Diagnosis: • + Clinical ... Antiphospholipid syndrome