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SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
pustulosis, pustular psoriasis ... , psoriasis vulgaris ... disease. ... SAPHO #Syndrome #Rheumatology ... #diagnosis #management
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Associated with Joint Pain ... infection • Lyme disease ... Plaques • Psoriasis ... arthritis • Psoriatic ... differential #diagnosis #rheumatology
Leg Pain - Differential Diagnosis Framework

Bone/Joint Causes of Leg Pain:
 • Fracture
 • Arthritis
 • Gout/pseudogout
Legg-Calve-Perthes disease ... Bursitis • IBD • Psoriasis ... thrombophlebitis Skin ... - HIV - Lyme disease ... ulcers - Shiny skin
Joint Disorders - Differential Diagnosis Algorithm
Monoarthritis
 • Septic
 • Crystalline
     - Gout
Molecular Mimicry” • Psoriatic ... arthritis - with the skin ... disorder psoriasis ... Inflammatory Bowel Disease ... systemic autoimmune disease
Extra-articular and Other Conditions Associated with Joint Pain

Eyes
  • Iritis or uveitis - Spondyloarthropathies, Sarcoidosis,
Associated with Joint Pain ... Onycholysis - Psoriatic ... • Pitting - Psoriatic ... Scleroderma Thickened skin ... differential #diagnosis #rheumatology
Seronegative Inflammatory Arthritis - Differential Diagnosis
 • Seronegative Rheumatoid Arthritis 
 • Infectious Arthritis: Viral, Bacterial,
Systemic Rheumatic Disease ... Sclerosis, Sjogren's Disease ... Sarcoidosis, Still's Disease ... Ankylosing Spondylitis, Psoriatic ... Differential #Diagnosis #rheumatology
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
trigger - Direct skin ... 50% of patients Skin ... Nausea, abdominal pain ... 1% of patients Skin ... Urticaria #diagnosis #rheumatology
Pustular Skin Lesions - Differential Diagnosis Framework

What are pustules?
• Pustules < 5-10 mm + pus
• Material
disease Pustular ... Pustular psoriasis ... disease in association ... with rheumatic pain ... Pustular psoriasis
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
Adult-Onset Still's Disease ... Arthralgia/arthritis, Skin ... autoinflammatory diseases ... #diagnosis #management ... #treatment #rheumatology
Pruritus - Generalized Differential Diagnosis Algorithm - Systemic and Primary Causes
== Primary Skin Lesions ==
Macules /
Causes == Primary Skin ... • Xerosis (dry skin ... dermatitis • Psoriasis ... Cholestatic liver disease ... syndrome Psychiatric Disease