16 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
enzyme, X-linked, Autoinflammatory ... , Somatic) Syndrome ... (MDS) Most met criteria ... #E1 #Xlinked #Autoinflammatory ... #Somatic #rheumatology
Consensus diagnostic criteria for asthma-COPD overlap syndrome (ACOS) in patients with airflow limitation. COPD=chronic obstructive pulmonary
Consensus diagnostic criteria ... asthma-COPD overlap syndrome ... Diagnosis #PCC #IM ... #Asthma #COPD #Criteria
Differential diagnosis of schistocytes / fragmentation hemolysis:
 • Thrombotic microangiopathies (TMA)
    - TTP
hemolytic-uremic syndrome ... anemia" • HELLP syndrome ... Catastrophic APLS BCM IM ... differential #diagnosis #hematology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
SAPHO Syndrome Summary ... SAPHO syndrome is ... Etiology unknown: Autoinflammatory ... antibiotics with antiinflammatory ... #Rheumatology #
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... Diagnosis Diagnostic Criteria ... for Behget's Syndrome ... the following 4 criteria ... #rheumatology
Drug Reaction with Eosinophilia and Systemic Symptoms (DRESS)
Definition: 
 • Severe adverse drug reaction, characterized by
Criteria for Diagnosis ... Hospital of Baltimore IM ... SinaiBmoreIMRes #DRESS #Syndrome
Hunter's Decision Rule (Sensitivity 84%, Specificity 97%), Sternbach's criteria - Need 3 of 10 symptoms: (Sensitivity
), Sternbach's criteria ... Diagnosis #EM #IM ... #Serotonin #Syndrome ... Algorithm #Sternbach #Criteria
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Macrophage Activation Syndrome ... Periodic fever syndromes ... hypersensitivity syndromes ... Histopathologic criteria ... #Rheumatology
NPSLE - Neurological and Psychiatric Manifestations of Systemic Lupus Erythematosus
 • Central: Aseptic meningitis, Cerebrovascular disease,
Neurological and Psychiatric ... Demyelinating syndrome ... Guillain-Barre syndrome ... #Neurological #Psychiatric ... Erythematosus #SLE #rheumatology
Diagnostic Criteria for Sweet Syndrome (Acute Febrile Neutrophilic Dermatosis)
Major criteria 
 1. Abrupt onset of tender
Diagnostic Criteria ... for Sweet Syndrome ... Dermatosis) Major criteria ... neutrophils #Sweet #Syndrome ... #Diagnosis #Hematology