10 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
enzyme, X-linked, Autoinflammatory ... thromboembolic disease ... (MDS) Most met criteria ... #E1 #Xlinked #Autoinflammatory ... #Somatic #rheumatology
Consensus diagnostic criteria for asthma-COPD overlap syndrome (ACOS) in patients with airflow limitation. COPD=chronic obstructive pulmonary
Consensus diagnostic criteria ... asthma-COPD overlap syndrome ... obstructive pulmonary disease ... Diagnosis #PCC #IM ... #Asthma #COPD #Criteria
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... Diagnosis Diagnostic Criteria ... for Behget's Syndrome ... the following 4 criteria ... #criteria #rheumatology
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
SAPHO syndrome is ... Etiology unknown: Autoinflammatory ... antibiotics with antiinflammatory ... osteoarticular and skin disease ... #Rheumatology #
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
Macrophage Activation Syndrome ... highly inflammatory disease ... Periodic fever syndromes ... Histopathologic criteria ... #Rheumatology
Drug Reaction with Eosinophilia and Systemic Symptoms (DRESS)
Definition: 
 • Severe adverse drug reaction, characterized by
Criteria for Diagnosis ... withdrawal • Mild disease ... treatment • Severe disease ... Hospital of Baltimore IM ... SinaiBmoreIMRes #DRESS #Syndrome
NPSLE - Neurological and Psychiatric Manifestations of Systemic Lupus Erythematosus
 • Central: Aseptic meningitis, Cerebrovascular disease,
Neurological and Psychiatric ... Cerebrovascular disease ... Demyelinating syndrome ... Guillain-Barre syndrome ... Erythematosus #SLE #rheumatology
Diagnostic Criteria for Sweet Syndrome (Acute Febrile Neutrophilic Dermatosis)
Major criteria 
 1. Abrupt onset of tender
Diagnostic Criteria ... for Sweet Syndrome ... inflammatory disease ... neutrophils #Sweet #Syndrome ... #Diagnosis #Hematology
Relapsing Polychondritis

What is it?
Recurrent inflammation of the cartilage in the body (Autoimmune disorder)

Who?
• Most frequently: 40
and fatigue Criteria ... immunologically mediated diseases ... • MAGIC syndrome ... Sarcoidosis • Behcet disease ... Polychondritis #rheumatology
Hemophagocytic Lymphohistiocytosis (HLH)

High mortality without prompt recognition and management. HLH is a critical diagnostic consideration in
hyperinflammatory syndrome ... ▪ Autoimmune diseases ... Diagnostic Criteria ... of 8 HLH-2004 criteria ... Diagnosis #Management #Hematology