169 results
Wilson's Disease - Pathogenesis and Clinical Features

#Wilsons #Disease #Pathophysiology #signs #symptoms #diagnosis #copper
Wilson's Disease ... Clinical Features #Wilsons ... #Disease #Pathophysiology ... #signs #symptoms ... #diagnosis #copper
Treatment of Wilson's Disease
 • D-penicillamine - Chelator, induces cupruria
 • Trientine - Chelator, induces cupruria
Treatment of Wilson's ... Disease • D-penicillamine ... absorption of copper #Wilsons ... #Disease #Treatment ... #management #pharmacology
Abnormal Liver Function Tests - Differential Diagnosis Algorithm for Transaminitis
Hepatocellular Pattern (ALT or AST > ALP):
Abnormal Liver Function ... - Differential Diagnosis ... Algorithm for Transaminitis ... Ischemia, AIH, Wilsons ... #diagnosis #hepatology
Elevated Liver Enzymes - Differential Diagnosis Algorithm
Severe ALT > 15x ULN
 • Viral
 • Drugs/Toxins
 •
Elevated Liver Enzymes ... - Differential Diagnosis ... Algorithm Severe ... • Cholestatic disease ... #Algorithm #Causes
Clinical Examination for Liver and Biliary Diseases
1) Hands: Clubbing, Dupuytren's contracture, Leuconychia, Bruising, Flapping tremor (hepatic
Examination for Liver ... Kayser-Fleischer rings in Wilson's ... physicalexam #cirrhosis #liver ... #disease #signs ... #diagnosis
Signs of Chronic Liver Disease ( Cirrhosis )

#Diagnosis #Cirrhosis #Signs #Symptoms #Hepatology
Signs of Chronic ... Liver Disease ( ... Cirrhosis ) #Diagnosis ... #Cirrhosis #Signs
Causes of Severe Acute Liver Injury
 - Ichemic hepatitis
 - Acute biliary obstruction
 - Drug-Induced liver
of Severe Acute Liver ... - Drug-Induced liver ... hepatitis - Wilson ... disease - Hemochromatosis ... Differential #Hepatology #Diagnosis
Causes of Acute Liver Injury - Differential Diagnosis
Hepatocellular - Liver Parenchyma
 • Infectious: Hepatitis C, A,
- Differential Diagnosis ... Hemochromatosis, Wilson's ... Disease, Alpha- ... #Differential #Diagnosis ... Causes #Acute #algorithm
Diagnostic Scoring System for Wilson's Disease
 - Kayser-Fleischer rings (2 points)
 - Neurological symptoms (2 points)
System for Wilson's ... Disease - Kayser-Fleischer ... anemia (1 point) - Liver ... very unlikely #Wilsons ... #Disease #Scoring
Hepatocellular Liver Injury - Differential Diagnosis Framework:
Liver Injury → liver test abnormalities without evidence of liver
- Differential Diagnosis ... Hemochromatosis, Wilson's ... disease, Alpha- ... HELLP, Celiac disease ... #hepatology #algorithm