37 results
Stevens-Johnson syndrome (SJS), Toxic epidermal necrolysis (TEN) and Overlap

 SJS-TEN overlap and TEN - Surface Epidermal
Stevens-Johnson syndrome ... Stevens #Johnsons #Syndrome ... #Distribution #SurfaceArea ... #Involvement
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... eosinophilia. and cardiac involvement ... Cryoglobulinemic vasculitis ... and Sjogren's syndrome ... • IgA vasculitis
Management of adult IgA Vasculitis (Henoch-Schönlein purpura) - Treatment algorithm for the management of IgAV patients
Henoch-Schönlein purpura) - Treatment ... according to organ involvement ... outcome of renal involvement ... Treatment remains ... HSP #Management #Treatment
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis ... manifestations - Skin involvement ... purpura - Renal involvement ... - Joint involvement ... neuropathy Treatment
BEE Syndromes - Immune-mediated conditions affecting the brain, eye, and ear

Visual or auditory symptoms in conjunction
BEE Syndromes - ... nervous system (CNS) involvement ... diagnosis and treatment ... • Sjögren syndrome ... ANCA-associated vasculitides
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Mucocutaneous lymph node syndrome ... : • Behçet Syndrome ... nervous system involvement ... • Cogan Syndrome ... Urinalysis (Renal involvement
Diagnosis of Cryoglobulinemia Vasculitis

1) Presence of cryoglobulin 
Circulating immunoglobulins that precipitate with cold temperature and dissolve
Cryoglobulinemia Vasculitis ... 3 types 2) Vasculitis ... Hyperviscosity syndrome ... arthritis • Renal Involvement ... Cryoglobulinemia #Vasculitis
Rheumatoid Arthritis Summary
MCP and PIP Involvement, Spares DIP, Carpal Tunnel, Sicca Syndrome, Epi/Scleritis, Heart Disease, Rheumatoid
Summary MCP and PIP Involvement ... Tunnel, Sicca Syndrome ... Disease, Rheumatoid Vasculitis ... Instability, Felty's Syndrome
Kawasaki Disease (Mucocutaneous Lymph Node Syndrome) 
An rare systemic acute febrile vasculitic syndrome. Aetiology unknown. 
Affects
Mucocutaneous Lymph Node Syndrome ... acute febrile vasculitic ... syndrome. ... developing cardiac involvement
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... panuveitis, retinal vasculitis ... MCC-small vessel vasculitis ... ulcers • Eye involvement ... Arthritis, AS Treatment