1394 results
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
Autoimmunity: • -MM/WM: Vasculitis ... normo-complementemic urticarial ... Hypergammaglobulinemic macular Vasculitis ... Paraproteinemias #Hematology
Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Hypocomplementemic Urticarial ... Vasculitis (HUV ... HUV 1) Chronic urticaria ... #Vasculitis #HUV ... Diagnosis #Management #Rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... bullae, Ulceration, Urticaria ... - Anti-C1q (Urticarial ... #skin #dermatology ... #rheumatology #
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Hypocomplementemic Urticarial ... Vasculitis C1q ... Hypocomplementemic #Urticarial ... #Vasculitis #HUV ... Pathophysiology #Rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... Hypocomplementemic Urticarial ... - Urticaria and ... cryoglobulinemia, urticarial ... differential #diagnosis #rheumatology
Vasculitis: In this instance, the vasculitic skin lesions were secondary to Haemophilus endocarditis.
Photo credit, Josh Fierer,
Vasculitis: In this ... instance, the vasculitic ... Clinical #Photo #Dermatology ... #SkinRash #Vasculitis
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of Vasculitis ... Vasculitis of ... hypocomplementary urticarial ... vasculitis ... Vessels #Diagnosis #Rheumatology
Severe Urticarial Skin Rash on Physical Exam

#Urticarial #Skin #Rash #PhysicalExam #clinical #video #dermatology #urticaria
Severe Urticarial ... Physical Exam #Urticarial ... clinical #video #dermatology ... #urticaria
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
Vasculitis - Break ... by large vessel vasculitis ... medium vessel vasculitis ... and small vessel vasculitis ... #Diagnosis #Rheumatology
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
Cold Urticaria Prevalence ... Chronic spontaneous urticaria ... Chronic inducible urticarias ... .14674 #Cold #Urticaria ... #diagnosis #rheumatology