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Diagnosis and Management of Hypocomplementemic Urticarial Vasculitis (HUV)

Diagnosis of HUV
1) Chronic urticaria 
2) Leukocytoclastic vasculitis 
3)
Hypocomplementemic Urticarial ... Vasculitis (HUV ... HUV 1) Chronic urticaria ... Leukocytoclastic vasculitis ... #Vasculitis #HUV
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... Leukocytoclastic Vasculitis ... bullae, Ulceration, Urticaria ... - Anti-C1q (Urticarial
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
pulmonary and renal ... Hypocomplementemic Urticarial ... - Urticaria and ... cryoglobulinemia, urticarial ... • Urinalysis (Renal
Pathophysiology of Hypocomplementemic Urticarial Vasculitis

C1q/anti-C1q antibiody ->
Immune Complex Formation - Complement Pathway Activation (C3a and C5a)
Hypocomplementemic Urticarial ... Vasculitis C1q ... Formation -> Vasculitis ... Hypocomplementemic #Urticarial ... #Vasculitis #HUV
Acute Kidney Injury (AKI) - Differential Diagnosis Framework
Pre-Renal:
 • Hypovolemia, Cardiorenal, Distributive Shock, HRS, Hypercalcemia, Renal
Framework Pre-Renal ... Hypercalcemia, Renal ... Medications Intra-Renal ... Emboli, Thrombosis, Vasculitis ... Differential #Diagnosis #nephrology
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
Pulmonary Renal ... ANCA-positive vasculitis ... ANCA-negative vasculitis ... IgA-associated vasculitis ... differential #diagnosis #nephrology
Causes of Acute Kidney Injury ( AKI ) - Prerenal, Renal, and Postrenal

PRE-RENAL 
Impaired perfusion: 
•
) - Prerenal, Renal ... Postrenal PRE-RENAL ... Small-vessel vasculitis ... Infection POST-RENAL ... #Differential #Nephrology
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of Vasculitis ... Vasculitis of ... ANCA-associated vasculitis ... hypocomplementary urticarial ... vasculitis
Intrinsic Renal Disease - Differential Diagnosis
Vascular:
 • Macrovascular: Renal artery occlusion, Fibromuscular disease
 • Microvascular: TTP/HUS,
Intrinsic Renal ... Macrovascular: Renal ... Athero-embolic, HTN, Vasculitis ... #Intrinsic #Renal ... #Disease #nephrology
Renal involvement in 35% of mixed cryoglobulinemia vasculitis 
Associated with : 
 • Absence of skin
Renal involvement ... cryoglobulinemia vasculitis ... TerrierBen #Renal ... Cryoglobulinemia #Vasculitis ... Cryoglobulinemic #Nephrology