18 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
VEXAS (Vacuoles, ... enzyme, X-linked, Autoinflammatory ... @MithuRheum #VEXAS ... #E1 #Xlinked #Autoinflammatory
Yao Syndrome vs VEXAS

Zhuoer Xie, MD @ZhuoerXie

#Yao #Syndrome #VEXAS #diagnosis #comparison #rheumatology
Yao Syndrome vs VEXAS ... Yao #Syndrome #VEXAS
VExUS - Venous Excess Ultrasound Score 

The Venous Excess UltraSound (VExUS) grading system prototypes combining inferior
VExUS - Venous Excess ... Excess UltraSound (VExUS ... 020-00163-w #VExUS
Causes of Leukocytosis and Leukopenia - Differential Diagnosis
 • Eosinophilia (AEC > 500, hypereosinophilia > 1500):
Marrow Failure, Autoinflammatory
Lancisi's sign in Severe Tricuspid Regurgitation - Physical Exam
Note the large systolic jugular venous wave caused
S-reversal on hepatic VExUS
Graft-Verus-Host Disease (GVHD) - Quick Reference Sheet
Multisystem disorder that is a common complication of allogeneic hematopoietic
Graft-Verus-Host
Causes of Pharyngitis - Differential Diagnosis
Infectious:
 • Bacterial: Group A Strep, Group B and C Strep,
Bowel Disease, Autoinflammatory
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
diseases : other autoinflammatory
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
Etiology unknown: Autoinflammatory ... antibiotics with antiinflammatory
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
dermatoses are autoinflammatory