38 results
Approach to Von Willebrand disease (VWD)

By Matthew Ho, MD PhD @MatthewHoMD

#VWD #Von #Willebrand #VonWillebrand #disease #hematology
Willebrand disease (VWD ... MatthewHoMD #VWD ... VonWillebrand #disease #hematology ... #algorithm #diagnosis
Pediatric Neutropenia Workup Algorithm

DOI: 10.1111/ijlh.13210

#Neutropenia #Workup #Algorithm #diagnosis #hematology #Pediatrics #peds
Pediatric Neutropenia ... Workup Algorithm ... Neutropenia #Workup #Algorithm ... #diagnosis #hematology ... #Pediatrics #peds
Inherited Qualitative Platelet Defects
Bernard-Soulier Syndrome
 • Defect of adhesion due to a lack of GP Ib/IX/V
Qualitative Platelet Defects ... of GP Ib/IX/V [vWF ... Thrombasthenia • Defect ... α-granules (contains vWF ... differential #diagnosis #hematology
Platelet disorders and Aggregometry
Glanzmann Thrombasthenia
 • Defective aggregation to all agonists except ristocetin
 • Normal platelet,
also be seen in vWD ... differentiate vWD ... BS by measuring vWF ... with qualitative defects ... Platelet #disorders #hematology
Cardiac Murmurs and Maneuvers

An algorithm demonstrating the effect of various maneuvers on systolic murmurs. 
TR, tricuspid
Maneuvers An algorithm ... demonstrating the effect ... aortic stenosis; VSD ... ventricular septal defect ... The effect of squatting
Causes of Thrombocytosis - Differential Diagnosis Algorithm
Spurious:
 • Artifact (redo CBC)
Autonomous:
 • Essential thrombocytosis
 • Polycythemia
Differential Diagnosis Algorithm ... Non malignant hematologic ... ITP • Rebound effect ... Differential #Diagnosis #Algorithm ... #Causes #Hematology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Thrombocytopenia • Platelet defects ... PURPURA: Platelet Defects ... syndrome Coagulation Defects ... Willebrand disease (VWD ... Differential #Diagnosis #hematology
Undifferentiated critical congenital heart disease: Patterns of Presentation 
Pink baby:
 • Presents at 1-6 mo
R shunt: PDA, VSD ... , AV canal defect ... catch blue baby defects ... Gray #Baby #Peds #Pediatrics
Hemolytic Anemias - Differential Diagnosis Algorithm

Signs of anemia and hemolysis:
 • ↓ Haptoglobin
 • ↑ LDH
Differential Diagnosis Algorithm ... Extrinsic RBC Defects ... : Membrane defects ... Differential #Diagnosis #Algorithm ... #hematology
Tetralogy of Falot on Chest X-Ray
Tetralogy of Falot comprises four defects -
1. Ventricular septal defect (VSD)
2.
comprises four defects ... Ventricular septal defect ... (VSD) 2. ... radiology #peds #pediatrics