1994 results
Hemolytic anemia in Wilson's disease

#Wilsons #Disease #hemolytic #anemia #Hematology #pathophysiology
Hemolytic anemia ... in Wilson's disease ... #Wilsons #Disease ... #hemolytic #anemia
Diagnostic Scoring System for Wilson's Disease
 - Kayser-Fleischer rings (2 points)
 - Neurological symptoms (2 points)
Scoring System for Wilson's ... Disease - Kayser-Fleischer ... Coombs-negative hemolytic anemia ... very unlikely #Wilsons ... #Disease #Scoring
Nail Disorders secondary to Systemic Diseases
Nail Fold Abnormality
 • SLE
 • Scleroderma
 • Dermatomyositis
Koilonychia - Spoon-shaped
secondary to Systemic Diseases ... Iron deficiency anemia ... • Any systemic disease ... Medications • Wilson's ... disease • Silver
Causes of Anemia in Cirrhosis - Differential Diagnosis Framework
LOW RETIC INDEX - ↓ PRODUCTION
 • Vitamin
Causes of Anemia ... Peptic ulcer disease ... syndrome, Spur cell anemia ... Hemolysis related to Wilson's ... disease, DIC-low
Diagnostic Framework for Hemolysis - Intravascular vs Extravascular Causes
Intravascular Hemolysis:
 • Mechanical Trauma (Microangiopathic hemolytic anemia):
Microangiopathic hemolytic anemia ... cold agglutin disease ... Hypersplenism, Wilson's ... disease, Copper ... diagnosis #hematology #anemia
Hemolysis - Differential Diagnosis Framework

1) Environment
  - Fragmentation
  - MAHA: TTP, HUS, DIC, HELLP
, Drugs, Liver Disease ... Defects: Sickle cell anemia ... Electrolytes: Wilson's ... disease, Hypophostphatemia
Jaundice and Kayser-Fleischer Rings in Wilson's Disease

#Jaundice #Kayser #Fleischer #Rings #Wilsons #Disease #clinical #video #ocular #physicalexam
Kayser-Fleischer Rings in Wilson's ... Disease #Jaundice ... Fleischer #Rings #Wilsons ... #Disease #clinical
Treatment of Wilson's Disease
 • D-penicillamine - Chelator, induces cupruria
 • Trientine - Chelator, induces cupruria
Treatment of Wilson's ... Disease • D-penicillamine ... absorption of copper #Wilsons ... #Disease #Treatment
Wing-Beating Tremor of Wilson's Disease

Characterized by low frequency, high amplitude, near arm tremor caused by continuous
Wing-Beating Tremor of Wilson's ... Disease Characterized ... Beating #Tremor #Wilsons ... #Disease #clinical
Low Alkaline Phosphatase - Hypophosphatasia 

Is Low Alkaline Phosphatase Of Clinical Importance?

ALP enzyme- Discovered in 1923
Low
Malnutrition • Wilson's ... disease • hypothyroidism ... • Pernicious anemia