18 results
Wing-Beating Tremor of Wilson's Disease

Characterized by low frequency, high amplitude, near arm tremor caused by continuous
Disease Characterized ... near arm tremor caused ... #Disease #clinical ... #video #neurology ... #copper #physicalexam
Wing-Beating Tremor of Wilson's Disease

Characterized by low frequency, high amplitude, near arm tremor caused by continuous
Disease Characterized ... near arm tremor caused ... #Disease #clinical ... #video #neurology ... #copper #physicalexam
Wing-Beating Tremor on Physical Exam

Seen in Wilson's disease, caused by copper toxicity (low ceruloplasmin)

#Wing #Beating #Tremor
disease, caused ... Beating #Tremor #PhysicalExam ... #clinical #video ... #neurology #wilsons ... #disease #copper
Hemolysis - Differential Diagnosis Framework

1) Environment
  - Fragmentation
  - MAHA: TTP, HUS, DIC, HELLP
MAHA: TTP, HUS, DIC ... Defects, Drugs, Liver ... Disease, PNH ... Electrolytes: Wilson's ... Differential #Diagnosis #hematology
Differential Diagnosis for Hemolytic Anemia
Intrinsic Causes:
 • Enzyme deficiencies ex. G6PD, pyruvate kinase 
 • Hemoglobinopathies
Anemia Intrinsic Causes ... : • Liver disease ... Intravascular Causes ... MAHA: TTP, HUS, DIC ... classification #hematology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
- DIC/TTP/HUS ... deficiency • Liver ... Purpura Fulminans (DIC ... Differential #Diagnosis #hematology ... #nonpalpable #dermatology
Diagnostic Framework for Hemolysis - Intravascular vs Extravascular Causes
Intravascular Hemolysis:
 • Mechanical Trauma (Microangiopathic hemolytic anemia):
Extravascular Causes ... intravascular coagulation (DIC ... Hypersplenism, Wilson's ... Extravascular #Causes ... differential #diagnosis #hematology
Wing-Beating Tremor of Wilson's Disease

Characterized by low frequency, high amplitude, near arm tremor caused by continuous
Disease Characterized ... near arm tremor caused ... #Disease #clinical ... #video #neurology ... #copper #physicalexam
Disseminated Intravascular Coagulation (DIC) Overview

Increased Clotting and Consumption of Clotting Factors

Findings:
 • Bleeding
 • Recent history
• Severe Liver ... Disease: - Impaired ... Treat primary cause ... #treatment #management ... #hematology
Causes of Thrombocytopenia and Platelet Disorders - Differential Diagnosis and Workup
History:
 - Prior platelet count, family
: INR/PT, aPTT(liver ... disease, decrease ... (CVID, WAS), (neurologic ... disease), HBsAg ... #Workup #hematology