48 results
Treatment of Wilson's Disease
 • D-penicillamine - Chelator, induces cupruria
 • Trientine - Chelator, induces cupruria
Treatment of Wilson's ... Disease • D-penicillamine ... of free serum copper ... #Wilsons #Disease ... #Treatment #management
Wing-Beating Tremor of Wilson's Disease

Characterized by low frequency, high amplitude, near arm tremor caused by continuous
Disease Characterized ... near arm tremor caused ... #Disease #clinical ... video #neurology #copper ... #physicalexam
Wing-Beating Tremor of Wilson's Disease

Characterized by low frequency, high amplitude, near arm tremor caused by continuous
Disease Characterized ... near arm tremor caused ... #Disease #clinical ... video #neurology #copper ... #physicalexam
Wing-Beating Tremor on Physical Exam

Seen in Wilson's disease, caused by copper toxicity (low ceruloplasmin)

#Wing #Beating #Tremor
Exam Seen in Wilson's ... disease, caused ... by copper toxicity ... Beating #Tremor #PhysicalExam ... #disease #copper
Von Willebrand Disease - Clinical Presentation, Diagnosis and Management

- Dr. Eric Strong @DrEricStrong - Strong Medicine
Von Willebrand Disease ... Diagnosis and Management ... VonWillebrand #Disease ... #Diagnosis #Management ... #hematology #treatment
Diagnostic Framework for Hemolysis - Intravascular vs Extravascular Causes
Intravascular Hemolysis:
 • Mechanical Trauma (Microangiopathic hemolytic anemia):
Extravascular Causes ... Hypersplenism, Wilson's ... disease, Copper ... Extravascular #Causes ... differential #diagnosis #hematology
Wing-Beating Tremor of Wilson's Disease

Characterized by low frequency, high amplitude, near arm tremor caused by continuous
Disease Characterized ... near arm tremor caused ... #Disease #clinical ... video #neurology #copper ... #physicalexam
Differential Diagnosis for Hemolytic Anemia
Intrinsic Causes:
 • Enzyme deficiencies ex. G6PD, pyruvate kinase 
 • Hemoglobinopathies
Anemia Intrinsic Causes ... : • Liver disease ... agents ex. lead, copper ... Intravascular Causes ... classification #hematology
Causes of Thrombocytosis - Differential Diagnosis Algorithm
Spurious:
 • Artifact (redo CBC)
Autonomous:
 • Essential thrombocytosis
 • Polycythemia
Causes of Thrombocytosis ... disorders • Celiac disease ... effect following treatment ... Diagnosis #Algorithm #Causes ... #Hematology
Myelodysplastic Syndrome (MD) - Diagnosis and Management Summary
myelo (marrow) -dys- (abnormal) -plastic (shape) = funny-shaped cells
Diagnosis and Management ... old, ~10,000 new cases ... acute leukemia Management ... only curative treatment ... #treatment #hematology