35 results
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
>>> MPA > eGPA ... ): eGPA, MPA >>> ... #differential # ... diagnosis #algorithm ... #rheumatology
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Polyangiitis (GPA ... Polyangiitis (MPA ... Polyangiitis (EGPA ... Guidelines #algorithm #rheumatology
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
polyangiitis (GPA ... polyangiitis (EGPA ... PR3 Anti-GBM disease ... #PR3 #Diagnosis ... #Rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
> PR3 60% • GPA ... • ANCA (Dx: GPA ... , EGPA, microscopic ... differential #diagnosis ... #rheumatology #
ILD of Known Cause - Differential Diagnosis
Exposure:
 • Occupational: Asbestosis, Silicosis, Hypersensitivity, Pneumonitis
 • Treatment Related:
Known Cause - Differential ... Diagnosis Exposure ... Granulomatous DX with Vasculitis ... : GPA, EGPA • ... #Diagnosis #interstitial
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Diagnosis Framework ... polyangiitis - EGPA ... - GPA Cutaneous ... : • Behcet Disease ... #dermatology #rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
Polyangiitis (GPA ... polyangiitis (GPA ... GPA causes disease ... Diagnosis: Vasculitis ... #Polyangiitis #GPA
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
polyangiitis (GPA ... polyangiitis (eGPA ... #differential # ... diagnosis #algorithm ... #rheumatology
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
Connective tissue disease ... (5%): PAN > GPA ... , EGPA • Solid ... signs #lesions #diagnosis ... pathology #lesions #differential
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Purpura - Differential ... - GPA - EGPA ... - MPA • CTD ... #Diagnosis #hematology ... #rheumatology #