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2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
Polyangiitis (GPA ... ) and Microscopic ... #Polyangiitis #GPA ... Management #rheumatology ... #algorithm #vasculitis
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
) and Microscopic ... Polyangiitis (MPA ... ) - ANCA Vasculitis ... #MPA #ANCA #Vasculitis ... #rheumatology
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Polyangiitis (GPA ... ), Microscopic Polyangiitis ... ACR2021 #Guidelines #algorithm ... #rheumatology
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Post-strep GN, Lupus ... ANCA (C-ANCA): GPA ... GPA Stanford Internal ... Glomerulonephritis #Vasculitis ... #rheumatology
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... polyangiitis (GPA ... ), microscopic polyangiitis ... Microscopic polyangiitis ... PR3 #Diagnosis #Rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
> PR3 60% • GPA ... purpura: strong sign ... • ANCA (Dx: GPA ... differential #diagnosis #rheumatology ... #classification
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... inflammation: • Microscopic ... polyangiitis (GPA ... differential #diagnosis #algorithm ... #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... Associated: - Microscopic ... polyangiitis - EGPA - GPA ... #skin #dermatology ... #rheumatology #
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... granulomatosis - microscopic ... - systemic lupus ... dermatomyositis #Size #Classification ... #Diagnosis #Rheumatology
Aortitis - Differential Diagnosis Framework
Non-Infectious Aortitis:
 • Vasculitides: Giant Cell Arteritis (GCA), Takayasu's arteritis, Cogan's Syndrome,
Cell Arteritis (GCA ... ANCA associated vasculitis ... (RA), Systemic lupus ... spondyloarthropathies (SPA ... Differential #Diagnosis #rheumatology