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A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
#Vessel #Size #Classification ... #ANCA #Differential
Rapidly Progressive Glomerulonephritis (RPGN) 
 - Loss of kidney function over a short period of tirne
cytoplasmic antibody (ANCA ... ) + • c-ANCA: ... staining • p-ANCA ... Glomerulonephritis #RPGN #Classification
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Associated - ANCA ... Granulomas - ANCA ... Granulomas - ANCA ... (MPO) - (C-ANCA ... #rheumatology #classification
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of ... small vessels - ANCA-associated ... dermatomyositis #Size #Classification
Vasculitis - Break down based on vessel size 
Distribution of vessel involvement by large vessel vasculitis,
basement membrane; ANCA ... Medium #Large #Classification
Serious Bacterial Illness (SBI):
1) UTI and pyelonephritis
Most common cause of SBI
Accounts for 3-8% of uncharacterized fevers
Female
suggested if: - ANC ... Diagnosis #Peds #EM #Classification
Pancreatic Fluid Collections - revised Atlanta Classification
Interstitial (85%):
 - Collections < 4 weeks - APFC (acute
revised Atlanta Classification ... Collections < 4 weeks - ANC ... Collections #Atlanta #Classification
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated ... - C-ANCA pattern ... antibody) - P-ANCA ... Hydralazine-induced ANCA ... @AnnKumfer #ANCA
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
Antibody) and ANCA ... polyangiitis - MPO>PR3 - ANCA ... 80-90%) > MPO - ANCA ... MPO: 75-80% - ANCA ... disease - MPO>PR3 - ANCA
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
DDX: • ANCA (Antineutrophil ... diagnosis #types #classification