61 results
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
- Diagnosis, causes ... Clinical manifestations ... - Skin involvement ... neuropathy Treatment ... with refractory disease
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
GPA causes disease ... • Pauci-immune vasculitis ... Rarely dominate the clinical ... Polyangiitis #GPA #dermatology ... rash #diagnosis #rheumatology
Pyoderma Gangrenosum: Autoimmune disorder resulting in a vasculitis which causes slowly progressive 
ulceration of the skin.
resulting in a vasculitis ... which causes slowly ... ulceration of the skin ... Images #Clinical ... #Photo #Dermatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Purpura, ischemic skin ... tract, and often causes ... - Skin, glomeruli ... Presentation - Systemic Symptoms ... differential #diagnosis #rheumatology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
association • M > F Clinical ... injury) • Neurologic ... oral ulcers in 12 ... Arthritis, AS Treatment ... #rheumatology #
BEE Syndromes - Immune-mediated conditions affecting the brain, eye, and ear

Visual or auditory symptoms in conjunction
conjunction with symptoms ... diagnosis and treatment ... Inflammatory causes ... ANCA-associated vasculitides ... BEE #Syndromes #neurology
Cold Urticaria
Prevalence - 0.05% in the population
Disease onset - Mostly 2nd to 4th decades of life
Causes
decades of life Causes ... and clinical associations ... and duration of symptoms ... angioedema Other symptoms ... Urticaria #diagnosis #rheumatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
Presentation: Systemic Symptoms ... , neurologic, and ... • Progressive symptoms ... cognitive impairment, neurologic ... tract, and often causes
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
episodes within a 12 ... Uveitis or retinal vasculitis ... - Skin lesions ... test Most Common Clinical ... Wide variety of skin
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
Somatic) Syndrome Clinical ... Syndrome: • Common Clinical ... nose chondritis, skin ... thromboembolic disease ... recurrent fevers, vasculitis