12 results
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
, small-vessel vasculitis ... ulceration • Ocular ... (panuveitis, retinal ... vasculitis) • ... : Giant retinal
Blurry Vision - Differential Diagnosis Framework

Anatomical Approach to Eye Disease:
1. Lids/Lashes
2. Extraocular Muscles/Motility
3. Conjunctiva/Sclera
4. Cornea
5. Anterior
Approach to Eye Disease ... Ocular Adverse Effects ... retinal vein occlusion ... - Retinal vein ... retinal vein occlusion
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Behcet's Syndrome ... Criteria for Behget's Syndrome ... or retinal vasculitis ... , retinal vasculitis ... ) • Arthritis (
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
and often causes arthritis ... , and ocular inflammation ... : • Behçet Syndrome ... gastrointestinal, and/or central ... • Cogan Syndrome
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
pulmonary and renal ... Angiitis of the Central ... • Behcet syndrome ... gastrointestinal, and/or central ... • Cogan syndrome
Facial Swelling - Differential Diagnosis Framework for Facial Edema

Infectious:
	• Dental abscess
	• Ludwig's angina
	• Vincent's angina
	• Cellulitis
	•
Adult-onset Still's disease ... Trauma: • Ocular ... internal jugular vein ... : • Morbihan disease ... Differential #Diagnosis #PhysicalExam
Transient Monocular Vision loss - Differential Diagnosis
Ischemia	
 - Large artery disease (atherothrombosis, embolus, dissection).
  -
- Large artery disease ... optic neuropathy, vasculitis ... ) Retinal vein ... Ocular causes - ... floaters obscuring central
Hematuria - Differential Diagnosis Framework

Gross Hematuria: Red/Dark urine
 • 1ml blood/liter urine can induce color change
basement membrane disease ... Diagnostic of GN or vasculitis ... of glomerular disease ... vein thrombosis ... vein between aorta
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
Erythematous, macular ... ANCA-associated vasculitis ... APLA/LAC: • Renal ... artery or vein ... thrombosis • Pelvic vein
Clinical Features of Systemic Lupus (SLE)
General: Fever (50%), Depression, Fatigue (75%), Weight loss (50%)
Eye: Sjögrens (15%)
Skin
Systemic Lupus (SLE) General ... Butterfly rash, Vasculitis ... of hip (rare), Arthritis ... Demyelinating syndromes ... disease (30%):