53 results
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... Interstitial lung disease ... • Eosinophilic ... polyangiitis - Asthma. eosinophilia ... Cryoglobulinemic vasculitis
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
• EGPA: - Eosinophilia ... (Granulomatous disease ... atherosclerotic disease ... most important diseases ... purpura: strong sign
Kawasaki Disease (Mucocutaneous Lymph Node Syndrome) 
An rare systemic acute febrile vasculitic syndrome. Aetiology unknown. 
Affects
Kawasaki Disease ... acute febrile vasculitic ... #Kawasaki #Disease ... #Features #Signs ... Diagnosis #Peds #Pediatrics
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... , small-vessel vasculitis ... polyangiitis (MPA), and eosinophilic ... polyangiitis - MPO>PR3 Eosinophilic ... PR3 Anti-GBM disease
Interstitial Lung Diseases (ILD)
Exposure-Related ILD (a.k.a. extrinsic allergic alveolitis): 
 • Hypersensitivity pneumonitis, Farmer's lung, Bird
Interstitial Lung Diseases ... Connective Tissue Disease ... Sarcoidosis • Vasculitis ... polyangiitis, Eosinophilic ... syndrome) • Eosinophilic
Cough - Diagnostic Schema

Infectious: URTI, LRTI, Bacterial, Viral
Irritant/Exposure: Allergic, Post-infectious, Pneumonitis, ACEi, PTX, Foreign Body
Airway Disease:
Foreign Body Airway Disease ... organ/systemic disease ... CHF, Autoimmune Vasculitis ... mycobacterial), Eosinophilic
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
semiology of Cutaneous Vasculitis ... • Drug-induced vasculitis ... Connective tissue disease ... • Necrotizing vasculitis ... dermatology #semiology #signs
Henoch Schonlein Purpura 
Typically a young boy. Often occurs following upper respiratory tract infection. A systemic
A systemic vasculitis ... Diagnosis #Peds #Pediatrics ... #Signs #Symptoms
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
atherosclerotic disease ... most important diseases ... purpura: Strong sign ... progressive) EGPA (Eosinophilic ... Polyangiitis): • Eosinophilia
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
ANCA-positive vasculitis ... (Eosinophilic granulomatosis ... ANCA-negative vasculitis ... IgA-associated vasculitis ... , Behcet disease