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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
progressing GN • New pulmonary ... glomerulonephritis and/or pulmonary ... • EGPA: - Eosinophilia ... arthritis, obstructive pulmonary ... Presentation - Systemic Symptoms
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
progressing GN • New pulmonary ... Presentation: Systemic Symptoms ... • Progressive symptoms ... progressive) EGPA (Eosinophilic ... Polyangiitis): • Eosinophilia
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Autoimmune ANCA vasculitis ... polyangiitis), EGPA (eosinophilic ... palpable purpura 2/2 vasculitis ... differential (check eosinophil ... or serologies + symptoms
Small Vessel Vasculitides
 • Granulomatosis with polyangiitis - Granulomatous manifestations (e.g., nasal crusting, destructive sinusitis, pulmonary
Small Vessel Vasculitides ... destructive sinusitis, pulmonary ... lung disease • Eosinophilic ... polyangiitis - Asthma. eosinophilia ... Cryoglobulinemic vasculitis
Eosinophilic Pneumonia
When to suspect Eosinophilic Pneumonia? Non-resolving pneumonia + BAL > 25% eosinophils + excluded more
Eosinophilic Pneumonia ... When to suspect Eosinophilic ... Constitutional Symptoms ... Consolidations AKA "inverse pulmonary ... Pneumonia #diagnosis #pulmonary
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated Vasculitis ... No Asthma and Eosinophilia ... Both asthma and eosinophilia ... and/or 10%) - Eosinophilic ... StanfordChiefs #ANCA #Vasculitis
Eosinophilic Esophagitis (EoE) - Spectrum of Response
Non-response:
 • Histology: Persistent eosinophilia, ≥ 15 eos/hpf
 • Symptoms:
Eosinophilic Esophagitis ... Histology: Persistent eosinophilia ... : Persistent symptoms ... Histology: Reduced eosinophilia ... score < 2 #Eosinophilic
Elevated Lactate Dehydrogenase (LDH) - Differential Diagnosis Framework

LDH is a cytoplasmic enzyme present in tissues throughout
Legionnaires disease • Pulmonary ... tumor burden) Vasculitis ... Polyarteritis nodosa • Eosinophilic ... associated with any symptoms
Differential Diagnosis of Pulmonary Eosinophilia
Infection:
 • Helminthic: Loffler syndrome (Ascaris, hookworm, Strongyloides), Tropical pulmonary eosinophilia (lymphatic
Differential Diagnosis of Pulmonary ... Eosinophilia Infection ... Strongyloides), Tropical pulmonary ... Acute chronic pulmonary ... #Pulmonary #Differential
More common & convincing pneumonia mimics 

Aspiration pneumonitis, 
Pulmonary vasculitis, 
Acute eosinophilic pneummia,  
Cryptogeric organizing
pneumonitis, Pulmonary ... vasculitis, Acute ... eosinophilic pneummia ... of idiopathic pulmonary ... fibrosis (IPF), Pulmonary