19 results
Role of G6PD in Protection against Oxidative Damage #Pathophys #Peds #Genetics #Honc #Favism #g6pd #NEJM
Role of G6PD in ... #Honc #Favism #g6pd
#Pathophys #Peds #Genetics #Honc #Favism #g6pd #NEJM
#Honc #Favism #g6pd
Drug-induced Hemolysis in G6PD Deficiency
Medicines and other substances likely to be UNSAFE in moderate to severe
Drug-induced Hemolysis in G6PD ... moderate to severe G6PD ... Kat_Watson #G6PD
Medications to Avoid in Patients with G6PD Deficiency Due to Risk of Hemolysis
 - Chloroquine (Aralen)*
Patients with G6PD ... Synthetase #G6PD
Peripheral Blood Smear Analysis
Hypochromia
Megaloblastic Anemia
Schistocytes: Microangiopathic hemolytic anemia (e.g. DIC, TTP, HUS)
Microspherocytes: Autoimmune hemolytic anemia
Sickled red
disease Bite cells: G6PD
Common RBC Inclusions and Associations
 • Howell Jolly Bodies: Hyposplenism, Asplenism, Severe hemolytic anemia
 • Heinz
Heinz Bodies: G6PD
Algorithmic Approach to Anemia - Differential Diagnosis Framework by MCV

Microcytic (MCV < 80) "TAILS":
 • Thalassemia
Spherocytosis, G6PD
Hemolytic Anemia - Differential Diagnosis Algorithm
Hereditary:
 • Peripheral blood smear + DAT + further History
 •
bodies, DAT (-) → G6PD
Hemolysis - Differential Diagnosis Framework

1) Environment
  - Fragmentation
  - MAHA: TTP, HUS, DIC, HELLP
Enzyme Defects: G6PD
Causes of Extravascular and Intravascular Hemolysis - Differential Diagnosis Algorithm
Extravascular - Spleen and RES-mediated hemolysis
 -
Defects • G6PD