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2021 ACR/VF Guidelines for Management of Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA)

#Granulomatosis #Polyangiitis #GPA
Guidelines for Management ... of Granulomatosis ... #MPA #ACR2021 #Management ... #rheumatology # ... algorithm #vasculitis
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated Vasculitis ... polyangiitis (GPA), microscopic ... involvement - PR3>MPO Microscopic ... PR3 Anti-GBM disease ... PR3 #Diagnosis #Rheumatology
Dermatologic Manifestations of Granulomatosis with Polyangiitis (GPA)

Skin involvement in granulomatosis with polyangiitis (GPA) is common and
• Pauci-immune vasculitis ... Polyarteritis nodosa • Microscopic ... vasculitis (inflamed ... Polyangiitis #GPA #dermatology ... rash #diagnosis #rheumatology
Vasculitis Management - ACR/VF 2021 Guidelines for Treatment & Management
 • Giant Cell Arteritis (GCA)
 •
Vasculitis Management ... Nodosa (PAN) • Granulomatosis ... Polyangiitis (GPA), Microscopic ... • Eosinophilic Granulomatosis ... @MithuRheum #Vasculitis
Autoantibodies and their Disease Associations
ANA - Non-specific; common in SLE, autoimmune hepatitis
Anti-CCP, Rheumatoid factor - RA
Anti-dsDNA
biliary cirrhosis (PBC ... c-ANCA - Vasculitis ... Wegener's granulomatosis ... p-ANCA - Vasculitis ... Microscopic polyangiitis
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of Vasculitis ... Vasculitis of ... - Wegener granulomatosis ... - microscopic ... Vessels #Diagnosis #Rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Granulomatosis with ... Polyangiitis (GPA) and Microscopic ... Polyangiitis (MPA) - ANCA Vasculitis ... Management Algorithm ... #Management #Treatment
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
ANCA-Associated Vasculitis ... : • Microscopic ... Renal-limited vasculitis ... antibodies #diagnosis #rheumatology ... #diseases
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
ANCA-positive vasculitis ... (Eosinophilic granulomatosis ... polyangiitis, Granulomatosis ... polyangiitis, Microscopic ... Investigations • Labs: CBC
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
PR3-ANCA): • Microscopic ... glomerulonephritis - Granulomatous ... (Granulomatous ... Lab Tests: • CBC ... Dx: GPA, EGPA, microscopic