9 results
Kawasaki Disease - Workup and Diagnostic Algorithm #Diagnosis #Management #Peds #Pediatrics #Kawasaki #Disease #Algorithm #CRASH #BURN
Kawasaki Disease ... Algorithm #Diagnosis ... #Management #Peds ... #Pediatrics #Kawasaki ... #CRASH #BURN #Mnemonic
THE LIMPING OR NON-WEIGHT BEARING CHILD PATHWAY

RED FLAGS - In all cases there are specific
markers which
FLAGS - In all cases ... suspicion of severe disease ... sweats, pallor, bruising ... Pathway #Child #Peds ... #Pediatrics #Diagnosis
Systemic Lupus Erythematosus (SLE) - Diagnosis and Management Summary
 • Epidemiology: 10-180/100,000, Typically Age 20-40, F:M
(SLE) - Diagnosis ... Manifestations: Malar rash ... Positive in 60-80% of cases ... Evolution: Chronic disease ... Erythematosus #Diagnosis
Drug Induced Lupus vs SLE
Drug Induced Lupus (DIL):
 • Epidemiology: -10% of all lupus cases, drug-dependent,
NPSLE rare, Malar rash ... Discontinuation of causal ... Evolution: Chronic disease ... #rheumatology #diagnosis ... #management
CNS Manifestations of Systemic Lupus Erythematosus (SLE)

Clinical Manifestations: Demyelinating Syndrome, Headache, Movement disorders, Seizure disorders, Aseptic
Cerebrovascular Disease ... autoantibodies that will cause ... permeability Diagnosis ... Erythematosus #SLE #CNS #neurology ... #management #treatment
Kawasaki Disease (KD) - Diagnosis and Management Summary

Kawasaki Disease (KD) is the most common vasculitis of
Conjunctivitis, Mucositis, Rash ... , Cough • +/-Nausea ... Polymorphous rash ... #rheumatology #pediatrics ... #diagnossi #management
Causes of Purpura or Easy Bruising in Children

Platelet count reduced, i.e. thrombocytopenia
 - Increased platelet destruction
Causes of Purpura ... SLE (systemic lupus ... Congenital heart disease ... #Causes #peds # ... pediatrics #diagnosis
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
• Systemic lupus ... manifestations: from easy bruising ... Petechial or purpuric rash ... Activation #Syndrome #Diagnosis ... #Management #Hematology
Posterior Reversible Encephalopathy Syndrome (PRES) Overview

Clinico-Radiological Syndrome, characterized by:
 • Headache
 • Seizures
 • Altered mental
Shock, Autoimmune disease ... the underlying cause ... Seizures: Treat with AEDs ... until cause identified ... #management #neurology