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Thrombotic Microangiopathies In Systemic Lupus Erythematosus

Dr. Laurent ARNAUD @Lupusreference

#TMAs #Thrombotic #Microangiopathies #Systemic #Lupus #Erythematosus #SLE #hematology
Microangiopathies In Systemic Lupus ... Erythematosus ... #Erythematosus ... #SLE #hematology ... differential #diagnosis #causes
EULAR/ACR Classification Criteria for Systemic Lupus Erythematosus
Clinical Domains:
 • Constitutional domain: Fever
 • Cutaneous domain: Non-scarring
EULAR/ACR Classification ... Erythematosus ... effusion, Acute pericarditis ... #Criteria #SLE ... #Erythematosus
SLE (Systemic Lupus Erythematosus)

Suspect:
Clinical evidence of (fatigue, rash, photosensitivity, inflammatory arthritis, weight loss, and fever) and
SLE (Systemic Lupus ... Skin Disease Classification ... • Asymptomatic pericarditis ... : Drug induced SLE ... SSA can rule in SLE
Top 10 situations when to think about lupus
1) Inflammatory joint pain (especially in the wrists and
4) Always with pericarditis ... sometimes « viral pericarditis ... children (pediatric SLE ... #diagnosis #sle ... #erythematosus #
Causes of Pericarditis - Differential Diagnosis Algorithm
Viral:
 • Coxsackie
 • Echovirus
 • Adenovirus
 • Epstein-Barr virus
Causes of Pericarditis ... arthritis • Systemic lupus ... erythematosus ... Diagnosis #Algorithm #Causes ... #Cardiology
Constrictive Pericarditis on POCUS Echocardiogram - Apical 3-Chamber View

Young Lupus patient admitted to hospital new onset
View Young Lupus ... What do you see ... could pinpoint the cause ... Lupus pericarditis ... Echocardiogram #clinical #cardiology
Constrictive Pericarditis on POCUS Echocardiogram - Subcostal View

Young Lupus patient admitted to hospital new onset HFpEF.
View Young Lupus ... What do you see ... could pinpoint the cause ... Lupus pericarditis ... Echocardiogram #clinical #cardiology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
• They can cause ... Cryoglobulins Cause ... (e.g. systemic lupus ... erythematosus ( ... diagnosis #types #classification
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
tract, and often causes ... erythematosus, ... reactions, and vaso-occlusive ... vasculitis, and SLE ... #rheumatology #classification
Causes of Hyperkalemia
l. Pseudohyperkalemia
  A Cellular efflux; thrombocytosis, erythrocytosis, leukocytosis, in vitro hemolysis
  B.
Causes of Hyperkalemia ... diseases: syßtemic lupus ... erythematosus ( ... High #Potassium #Classification ... #Causes