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Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
Vasculitis and Vasculitides ... : ANCA Associated ... - ANCA specific ... Vasculitis: + MPO-ANCA ... disease): • Takayasu
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... 50% Cutaneous Vasculitis ... Leukocytoclastic Vasculitis ... • ANCA Associated ... arteritis • Takayasu's
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Classification of Vasculitis ... Vasculitis of ... arteritis) - Takayasu ... small vessels - ANCA-associated ... vasculitis
Aortitis - Differential Diagnosis Framework
Non-Infectious Aortitis:
 • Vasculitides: Giant Cell Arteritis (GCA), Takayasu's arteritis, Cogan's Syndrome,
Non-Infectious Aortitis: • Vasculitides ... Arteritis (GCA), Takayasu's ... Nodosa (PAN), ANCA ... associated vasculitis
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
GRANULOMATOUS DISEASE): Takayasu ... : ANCA Associated ... Pauci Immune (ANCA ... No Granulomas (ANCA ... (-Granulomas) ANCA
Highlighted Conditions With Arteritis or Periarteritis of the Coronaries
Takayasu's arteritis:
 - Onset < 40 yrs
 -
the Coronaries Takayasu's ... Mononeuritis multiplex ANCA ... vasculitis: - ... Leukocytoclastic vasculitis
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
Vasculitis A group ... , small-vessel vasculitis ... Levamisole-induced vasculitis ... vasculitis - MPO ... #Associated #Vasculitis
A System for Vasculitides 

#Diagnosis #IM #Rheum #Vasculitis #Small #Medium #Large #Vessel #Size #Classification #ANCA #Differential
A System for Vasculitides ... Diagnosis #IM #Rheum #Vasculitis ... Classification #ANCA
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
Antibody) and ANCA ... Vasculitis: • ... 80-90%) > MPO - ANCA ... Renal-limited vasculitis ... Antinuclear #Antibody #ANCA
ANCA Associated Vasculitis (AAV) - Auto-antibodies and Differential Diagnosis

MPA → usually p-ANCA
GPA → usually c-ANCA
EGPA →
Vasculitis (AAV) ... Vasculitis Levamisole-Induced ... ANCA Vasculitis ... Vasculitis By ... #Vasculitis #AAV