13 results
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
polyangiitis (GPA ... ), microscopic polyangiitis ... polyangiitis (EGPA ... involvement - PR3>MPO Microscopic ... #Diagnosis #Rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
) and Microscopic ... ) - ANCA Vasculitis ... #Microscopic #Polyangiitis ... #MPA #ANCA #Vasculitis ... Guidelines #algorithm #rheumatology
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... inflammation: • Microscopic ... polyangiitis (GPA ... StanfordChiefs #ANCA ... diagnosis #algorithm #rheumatology
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
cases • Sjögren syndrome ... Vasculitis: • Microscopic ... 80-90%) > MPO - ANCA ... MPO: 75-80% - ANCA ... antibodies #diagnosis #rheumatology
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
): • Microscopic ... VASCULITIS: • Behçet Syndrome ... • Cogan Syndrome ... microscopic polyarteritis ... differential #diagnosis #rheumatology
Autoantibodies and their Disease Associations
ANA - Non-specific; common in SLE, autoimmune hepatitis
Anti-CCP, Rheumatoid factor - RA
Anti-dsDNA
La) - Sjogren's syndrome ... Graves' disease c-ANCA ... granulomatosis p-ANCA ... Microscopic polyangiitis ... diagnosis #table #rheumatology
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis • ANCA ... Associated: - Microscopic ... - GPA Cutaneous ... Disease • Cogan syndrome ... #dermatology #rheumatology
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Pulmonary Renal Syndromes ... Summary Autoimmune ANCA ... (microscopic polyangiitis ... Auto-antibodies: ANCA ... FINDINGS: • U/A: microscopic
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
small vessels - ANCA-associated ... granulomatosis - microscopic ... Churg-Strauss syndrome ... - Sjögren syndrome ... Vessels #Diagnosis #Rheumatology
Cryoglobulinemia Summary

Cryoglobulins:
 • Cryoglobulins are Igs in the serum that precipitate in vitro at temperatures below
Hyperviscosity Syndrome ... DDX: • ANCA (Antineutrophil ... associated vasculitis - GPA ... , EGPA, microscopic ... classification #rheumatology