11 results
Treatment of Non-hepatitis C virus Cryoglobulinemia Vasculitis - French Vasculitis Study Group

MONOCLONAL CRYOGLOBULINEMIA (TYPE 1) 
IgM
Treatment of Non-hepatitis ... - French Vasculitis ... /or refractory disease ... TerrierBen #NonHCV ... #Management #Rheumatology
Non-HCV infectious mixed cryoglobulinemia vasculitis - Diagnosis, causes and management - French Vasculitis Study Group

< 5%
cryoglobulinemia vasculitis ... neuropathy Treatment ... with refractory disease ... TerrierBen #NonHCV ... #Rheumatology #
Polyarteritis Nodosa (PAN) - Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Severe Disease → Remission
Nodosa (PAN) - Vasculitis ... • Non-Severe Disease ... immunosuppressive agent (e.g ... #Management #Treatment ... Guidelines #algorithm #rheumatology
Behcet's Syndrome - Diagnosis
Diagnostic Criteria for Behget's Syndrome (International Study Group for Behget's Disease):
 • Recurrent,
Diagnosis Diagnostic Criteria ... the following 4 criteria ... Uveitis or retinal vasculitis ... retinal vasculitis ... #rheumatology
Kawasaki Disease (KD) - Diagnosis and Management Summary

Kawasaki Disease (KD) is the most common vasculitis of
the most common vasculitis ... Diagnostic Criteria ... #KD #vasculitis ... #rheumatology # ... diagnossi #management #treatment
IgG4-Related Disease
Clinical history:  Man, 60 years, multiorgan involvement, unique or multiple inflammatory pseudotumor
4 phenotypes:
 •
IgG4-Related Disease ... No necrosis, No vasculitis ... Glucocorticoids (0.6 mg/kg ... IgG4 #Related #Disease ... #rheumatology
Macrophage Activation Syndrome (MAS)
Classified among the secondary or acquired forms of haemophagocytic lymphohistiocytosis (sHLH)

What?
A subset of
• Infection (eg ... Histopathologic criteria ... Treatment: • Corticosteroids ... Diagnosis #Management #Hematology ... #Rheumatology
Adult Onset Still's Disease
Systemic inflammation with urticarial rash.
Rash: 
 • Nonpruritic, evanescent (correlates with time of
Onset Still's Disease ... Treatment - Mild ... : NSAIDS Treatment ... Prednisone 0.5-1mg/kg ... AOSD #diagnosis #rheumatology
IGG-4 RELATED DISEASE

WHAT?
 • A chronic, immune-mediated fibroinflammatory disease with tumefactive infiltration of IgG4+ plasma cells
aortitis, mimics vasculitis ... • Essential Criteria ... 2019 ACR/EULAR Criteria ... Prednisone: 0.6 mg/kg ... Diagnosis #Management #Rheumatology
Monoclonal Gammopathy of Renal Significance (MGRS)

MGRS
• MGRS refers to kidney disease caused by nephrotoxic monoclonal immunoglobulins
does not meet criteria ... for hematologic ... or evolve into hematologic ... formation causing vasculitis ... microangiopathy Treatment