11 results
VEXAS (Vacuoles, E1 enzyme, X-linked, Autoinflammatory, Somatic) Syndrome
Clinical Syndrome:
 • Common Clinical Features: alveolitis, ear and
VEXAS (Vacuoles, E1 ... enzyme, X-linked, Autoinflammatory ... • UBA1 = major E1 ... Syndrome #Vacuoles #E1 ... #Xlinked #Autoinflammatory
Outcomes in Severe Hyponatremia Treated With and Without Desmopressin.

Am J Med. 2018 Mar;131(3):317.e1-317.e10. doi: 10.1016/j.amjmed.2017.09.048. Epub
Mar;131(3):317.e1
Causes of Leukocytosis and Leukopenia - Differential Diagnosis
 • Eosinophilia (AEC > 500, hypereosinophilia > 1500):
Marrow Failure, Autoinflammatory
Causes of Pharyngitis - Differential Diagnosis
Infectious:
 • Bacterial: Group A Strep, Group B and C Strep,
Bowel Disease, Autoinflammatory
Adult-Onset Still's Disease
Clinical triad: Fever, Arthralgia/arthritis, Skin rash ± odynophagia
+ Biological inflammation: Increased neutrophils, Hyperferritinemia, decreased
diseases : other autoinflammatory
SAPHO Syndrome Summary

What?
SAPHO syndrome is a rare chronic inflammatory disorder of bone, joint, and skin characterized
Etiology unknown: Autoinflammatory ... antibiotics with antiinflammatory
Sweet Syndrome

Acute febrile neutrophilic dermatosis (Sweets Syndrome) is a skin condition characterized by fever and inflamed
dermatoses are autoinflammatory
A Comparison of Headache Treatment in the Emergency Department: Prochlorperazine Versus Ketamine
Zitek T, Gates M, Pitotti
2018;71(3):369-77 e1
Classification for benign biliary strictures
Bismuth classification
I - Low CHD stricture, > 2 cm distal to hilum
II
extrahepatic ducts E1
Pyoderma Gangrenosum (PG)
50 M Crohn’s dz had a small pustule on the ankle 4 mo ago
considered an autoinflammatory