21 results
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
Vasculitis A group ... , small-vessel vasculitis ... - C-ANCA pattern ... PR3 Anti-GBM disease ... PR3 #Diagnosis #Rheumatology
ANA (Antinuclear Antibody) and ANCA (Antineutrophil cytoplasmic antibodies)
 • Systemic lupus erythematosus
   1. Anti-dsDNA
) • Systemic lupus ... Vasculitis: • ... Renal-limited vasculitis ... antibodies #diagnosis #rheumatology ... #diseases
Classification of Vasculitis 
Vasculitis of large vessels 
 - Arteritis temporalis (giant-cell arteritis) 
 - Takayasu
Vasculitis of ... small vessels - ANCA-associated ... - Wegener granulomatosis ... - systemic lupus ... Vessels #Diagnosis #Rheumatology
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
granulomatosis ... polyangiitis, Granulomatosis ... vasculitis, Behcet ... Complex: Systemic lupus ... testing: anti-ANCA
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
glomerulonephritis - Granulomatous ... inflammation Others: • Lupus ... (Granulomatous ... such as systemic lupus ... differential #diagnosis #rheumatology
Autoantibodies and their Disease Associations
ANA - Non-specific; common in SLE, autoimmune hepatitis
Anti-CCP, Rheumatoid factor - RA
Anti-dsDNA
Associations ANA ... c-ANCA - Vasculitis ... Wegener's granulomatosis ... p-ANCA - Vasculitis ... diagnosis #table #rheumatology
Granulomatosis with Polyangiitis (GPA) and Microscopic Polyangiitis (MPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021
Granulomatosis with ... Polyangiitis (MPA) - ANCA ... Vasculitis Management ... Polyangiitis #MPA #ANCA ... #Treatment #ACR2021
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Eosinophilic Granulomatosis ... Polyangiitis (EGPA) - ANCA ... Vasculitis Management ... #Polyangiitis #ANCA ... #Treatment #ACR2021
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
(GRANULOMATOUS ... /hr • Biopsy: Granulomatous ... (Eosinophilic Granulomatosis ... PR3 60/ GPA (Granulomatosis ... Differential #Diagnosis #Rheumatology
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Post-strep GN, Lupus ... involvement: Anti-GBM Disease ... (C-ANCA): GPA > ... Glomerulonephritis #Vasculitis ... diagnosis #algorithm #rheumatology