11 results
Autoimmune Hemolytic Anemia (AIHA) Treatment
Warm AIHA:
1) Steroids - 1-2 mg/kg prednisone daily
   • Until
Anemia (AIHA) Treatment ... esp if severe disease ... azathioprine Cold ... Polyclonal: - Infection ... #hematology
Diagnostic Framework for Hemolysis - Intravascular vs Extravascular Causes
Intravascular Hemolysis:
 • Mechanical Trauma (Microangiopathic hemolytic anemia):
- Autoimmune (AIHA ... - Autoimmune (AIHA ... Mycoplasma pneumoniae infection ... spherocytosis) • Infections ... differential #diagnosis #hematology
Cold Agglutinin Disease

3 Types of Cold Sensitive Antibodies:
  1. Cold Agglutinins (CAD)
  2. Donath-Landsteiner
women • 15% of AIHA ... Agglutinin Syndrome (CAS ... - Due to Viral infection ... #hemolytic #anemia ... #hematology #diagnosis
Hemolysis - Differential Diagnosis Framework

1) Environment
  - Fragmentation
  - MAHA: TTP, HUS, DIC, HELLP
Hemolysis - Differential ... Autoimmune: Warm AIHA ... , Cold AIHA, Transfusion ... Internal (RBC) - Infections ... Differential #Diagnosis #hematology
Differential Diagnosis for Hemolytic Anemia
Intrinsic Causes:
 • Enzyme deficiencies ex. G6PD, pyruvate kinase 
 • Hemoglobinopathies
Causes: • Liver disease ... Hypersplenism • AIHA ... : warm, cold, drug ... induced • Infections ... classification #hematology
Listeriosis Summary - Listeria Monocytogenes
Pathogen: Listeria Monocytogenes - Gram-positive rod, Aerobic, facultative anaerobe, motile, beta-hemolytic, Non-spore-forming
Risk
, motile, beta-hemolytic ... PPI use Food: Cold ... Pregnancy • CNS ... ) • CSF (CNS Infection ... infectiousdiseases #treatment
Listeriosis Summary - Listeria Monocytogenes
Pathogen: Listeria Monocytogenes - Gram-positive rod, Aerobic, facultative anaerobe, motile, beta-hemolytic, Non-spore-forming
Risk
, motile, beta-hemolytic ... PPI use Food: Cold ... Pregnancy • CNS ... ) • CSF (CNS Infection ... infectiousdiseases #treatment
Paraproteinemias

Entities That Can Feature A Monoclonal Protein/M Component:
• MM
• WM
• MGUS
• MGCS
• MGRS
• Splenic Marginal Zone
• Heavy Chain disease ... Scleromyxedema (CNS ... Coagulopathy) SMZL: • AIHA ... • Coombs (-) hemolytic ... Paraproteinemias #Hematology
Behçet's Syndrome
Systemic disease associated with inflammation of multiple organs, small-vessel vasculitis and large-vessel vasculopathy
Epidemiology:
 • Young
matter, spinal cord ... basal ganglia, CNS ... Arthritis, AS Treatment ... monoclonal TNF-aIpha ... signs #symptoms #rheumatology
Bronchiectasis - Summary

What?
• Bronchiectasis is derived from the Greek words bronckos meaning airway and ectasis meaning
Connective tissue diseases ... obstruction • COPD ... , in advanced disease ... mycobacteria Treatment ... the airway • Treating