8291 results
Von Willebrand Disease Classification
Type 1 (Accounts for ~3/4 of cases):
 • Defect: Quantitative defect (i.e. not
of cases): • Defect ... : Quantitative defect ... : Qualitative defect ... Bleeding: Severe (Clinically ... Types #diagnosis #hematology
Central Retinal Artery Occlusion: Pathogenesis and clinical findings
 • Inflammatory Disease: (i.e. GCA, SLE, GPA) ->
Pathogenesis and clinical ... arrhythmias, congenital defects ... anti-coagulation • Hematologic
Pathophysiology of Hemolytic Anemia
 - Defects in RBC internal contents (thalassemia, hemoglobinopathies, and metabolic defects)
 -
Hemolytic Anemia - Defects ... and metabolic defects ... ) - Defects in ... rnembranes - Defects ... Hemolytic #Anemia #hematology
Clinical features of focal cortical brain lesions in a right-handed individual

Frontal, either:  
Intellectual impairment, 
Personality
Clinical features ... Homonymous field defect ... Homonymous field defect ... Homonymous field defect ... Visual field defects
Hemolytic Anemias - Differential Diagnosis Algorithm

Signs of anemia and hemolysis:
 • ↓ Haptoglobin
 • ↑ LDH
Extrinsic RBC Defects ... Intrinsic RBC Defects ... : Membrane defects ... Diagnosis #Algorithm #hematology
Inherited Qualitative Platelet Defects
Bernard-Soulier Syndrome
 • Defect of adhesion due to a lack of GP Ib/IX/V
Qualitative Platelet Defects ... Bernard-Soulier Syndrome • Defect ... Thrombasthenia • Defect ... Related Disorder • Defect ... differential #diagnosis #hematology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Thrombocytopenia • Platelet defects ... PURPURA: Platelet Defects ... syndrome Coagulation Defects ... Differential #Diagnosis #hematology ... #rheumatology #
Hemolysis - Differential Diagnosis Framework

1) Environment
  - Fragmentation
  - MAHA: TTP, HUS, DIC, HELLP
Non-immune: Membrane Defects ... Spiders - Enzyme Defects ... - Hemoglobin Defects ... Differential #Diagnosis #hematology
Causes of Extravascular and Intravascular Hemolysis - Differential Diagnosis Algorithm
Extravascular - Spleen and RES-mediated hemolysis
 -
Abnormal Hgb & Hgb Defects ... Hgb - Membrane Defects ... - RBC Enzyme Defects ... Algorithm #Causes #Hematology
Hypereosinophilia and Hypereosinophilic Syndrome

 • Secondary Hypereosinophilic Syndrome
 • Clinically Relevant HES Variants
 • When to
Hypereosinophilic Syndrome • Clinically ... suspect underlying hematologic ... Syndrome #HES #Hematology