11 results
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... polyangiitis (GPA ... StanfordChiefs #ANCA ... #diagnosis #algorithm
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated ... polyangiitis (GPA ... ), and eosinophilic ... polyangiitis - MPO>PR3 Eosinophilic ... #Associated #Vasculitis
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Glomerulonephritis • With associated ... (C-ANCA): GPA > ... MPO-ANCA (P-ANCA ... Glomerulonephritis #Vasculitis ... differential #diagnosis #algorithm
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: ANCA Associated ... : - Eosinophilia ... Hydralazine-Induced ANCA-Associated ... Vasculitis: + MPO-ANCA ... purpura: strong sign
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
Vasculitis Involving ... • ANCA Associated ... polyangiitis - EGPA ... - GPA Cutaneous ... #skin #dermatology
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Eosinophilic Granulomatosis ... ) - ANCA Vasculitis ... Management Algorithm ... #Eosinophilic # ... #Polyangiitis #ANCA
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
(5%): PAN > GPA ... , EGPA • Solid ... #dermpath #dermatology ... #semiology #signs ... manifestations #pathology
Purpura - Differential Diagnosis Framework

Non-blanchable, dark red to purple, hemorrhagic skin lesions that result from leakage
Cryoglobulinemia (MIXED) • ANCA ... associated small ... - GPA - EGPA ... Associated - ... #nonpalpable #dermatology
Vasculitis - Differential Diagnosis Framework

When to Consider Vasculitis:
• Purpura, ischemic skin lesions
• Mononeuritis multiplex
• Hematuria, proteinuria,
purpura: Strong sign ... : ANCA Associated ... (Eosinophilic Granulomatosis ... Polyangiitis): • Eosinophilia ... MPO > PR3 60/ GPA
Skin Conditions Associated with Joint Pain

Rash
	• Human parvovirus B19 infection

Malar rash
	• SLE
	• Human parvovirus B19 infection
	•
Skin Conditions Associated ... Amyloidosis • Eosinophilic ... Hypersensitivity vasculitis ... Sarcoidosis • GPA ... Sarcoidosis #dermatology