18 results
ANCA-Associated Vasculitis
There are many definitions, but most come down to the presence of granulomas (pathologically or
ANCA-Associated ... Vasculitis There ... polyangiitis (GPA ... #Vasculitis #differential ... #diagnosis #algorithm
ANCA-Associated Vasculitis
A group of necrotizing, small-vessel vasculitis without immune complex deposition. Complement levels are normal due
ANCA-Associated ... polyangiitis (GPA ... ), and eosinophilic ... polyangiitis - MPO>PR3 Eosinophilic ... #Associated #Vasculitis
ANCA Associated Vasculitis (AAV) - Auto-antibodies and Differential Diagnosis

MPA → usually p-ANCA
GPA → usually c-ANCA
EGPA →
ANCA Associated ... Auto-antibodies and Differential ... c-ANCA EGPAANCA ... ANCA Vasculitis ... #Differential #
Rapidly Progressive Glomerulonephritis (RPGN)
RPGN has three primary pathophysiologic causes differentiated by immunofluorescence

Immune Complex Mediated (granular staining):
Glomerulonephritis • With associated ... (C-ANCA): GPA > ... Glomerulonephritis #Vasculitis ... #differential # ... diagnosis #algorithm
Vasculitis and Vasculitides - Differential Diagnosis Framework

When to Consider Vasculitis:
 • Purpura, ischemic skin lesions
 •
: ANCA Associated ... : - Eosinophilia ... > PR3 60% • GPA ... Hydralazine-Induced ANCA-Associated ... purpura: strong sign
Eosinophilic Granulomatosis with Polyangiitis (EGPA) - ANCA Vasculitis Management Algorithm - ACR/VF 2021 Guidelines
 • Active
Eosinophilic Granulomatosis ... ) - ANCA Vasculitis ... Management Algorithm ... #Eosinophilic # ... #Polyangiitis #ANCA
Vasculitis Involving the Skin - Differential Diagnosis Framework

Primary: 50% Cutaneous Vasculitis: Leukocytoclastic Vasculitis
Secondary: CTD: SLE, RA
the Skin - Differential ... • ANCA Associated ... polyangiitis - EGPA ... - GPA Cutaneous ... #rheumatology #differential
Dermatological semiology of Cutaneous Vasculitis 

Clinicopathologic correlations
 • Purpura, papules, pustules, necrosis: involvement of small vessels
(5%): PAN > GPA ... , EGPA • Solid ... dermatology #semiology #signs ... manifestations #pathology ... #lesions #differential
Pulmonary Renal Syndrome

Definition: Diffuse alveolar hemorrhage + Glomerulonephritis
Presentation (Pulmonary and renal manifestations can occur weeks apart):
symptomatology Differential ... vasculitis (Eosinophilic ... vasculitis (IgA-associated ... vasculitis, Behcet ... Renal #Syndrome #differential
Pulmonary Renal Syndromes - OnePager Summary
Autoimmune ANCA vasculitis (AAV): GPA (granulomatous with polyangiitis), EGPA (eosinophilic granulomatosis
Summary Autoimmune ANCA ... vasculitis (AAV ... ): GPA (granulomatous ... (eosinophilic granulomatosis ... (check eosinophil